Clinical manifestations and management of life-threatening bleeding in the largest group of patients with severe factor XIII deficiency

International Journal of Hematology

Volumn 100, Issue 5, 2014, Pages 443-449

  Naderi, Majid ^a   Dorgalaleh, Akbar ^b   Alizadeh, Shaban ^b   Tabibian, Shadi ^b   Hosseini, Soudabeh ^c   Shamsizadeh, Morteza ^d   Bamedi, Taregh ^a  

^a ZAHEDAN UNIVERSITY OF MEDICAL SCIENCES   (Iran)

^b TEHRAN UNIVERSITY OF MEDICAL SCIENCES   (Iran)

^c IRAN UNIVERSITY OF MEDICAL SCIENCES   (Iran)

^d SHAHROUD UNIVERSITY OF MEDICAL SCIENCES   (Iran)

Author keywords

Clinical manifestation; Factor XIII deficiency; Hemorrhagic disorder

Indexed keywords

ARGININE; BLOOD CLOTTING FACTOR 13 CONCENTRATE; BLOOD CLOTTING FACTOR 13A; TRYPSIN; BLOOD CLOTTING FACTOR 13;

ADOLESCENT; ADULT; APHASIA; ARTICLE; BEHAVIOR DISORDER; BLEEDING; BLOOD CLOTTING FACTOR 13 DEFICIENCY; BRAIN HEMORRHAGE; CHILD; CLINICAL FEATURE; CONTROLLED STUDY; DEVELOPMENTAL DISORDER; DOSE RESPONSE; DRUG MEGADOSE; FEMALE; GENE MUTATION; GENOTYPE; GESTATION PERIOD; HEMATOMA; HOMOZYGOTE; HUMAN; IRAN; MAJOR CLINICAL STUDY; MALE; NEWBORN; NEWBORN MONITORING; SPONTANEOUS ABORTION; TREATMENT DURATION; TREATMENT OUTCOME; UMBILICAL BLEEDING; YOUNG ADULT; ABORTION, SPONTANEOUS; COMPLICATION; DISEASE MANAGEMENT; FACTOR XIII DEFICIENCY; GENETICS; HEMORRHAGE; INTRACRANIAL HEMORRHAGES; MUTATION; NUCLEOTIDE SEQUENCE; PRESCHOOL CHILD;

ABORTION, SPONTANEOUS; ADOLESCENT; ADULT; CHILD; CHILD, PRESCHOOL; DISEASE MANAGEMENT; DNA MUTATIONAL ANALYSIS; FACTOR XIII; FACTOR XIII DEFICIENCY; FEMALE; HEMORRHAGE; HUMANS; INFANT, NEWBORN; INTRACRANIAL HEMORRHAGES; MALE; MUTATION; YOUNG ADULT;

EID: 84919916817     PISSN: 09255710     EISSN: 18653774     Source Type: Journal    
DOI: 10.1007/s12185-014-1664-1     Document Type: Article

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