Wolman disease associated with hemophagocytic lymphohistiocytosis: attempts for an explanation

European Journal of Pediatrics

Volumn 173, Issue 10, 2014, Pages 1391-1394

  Taurisano, Roberta ^a   Maiorana, Arianna ^a   De Benedetti, Fabrizio ^b   Dionisi Vici, Carlo ^a   Boldrini, Renata ^a   Deodato, Federica ^a  

^a BAMBINO GESÙ CHILDREN S HOSPITAL   (Italy)

^b IRCCS   (Italy)

Author keywords

Cholesterol crystal; Hemophagocytic lymphohistiocytosis; Inflammasome; Wolman disease

Indexed keywords

ALANINE AMINOTRANSFERASE; ASPARTATE AMINOTRANSFERASE; BILIRUBIN; CHOLESTEROL ESTER; FERRITIN; FIBRINOGEN; LACTATE DEHYDROGENASE; PROTHROMBIN; TRIACYLGLYCEROL; BIOLOGICAL MARKER; INFLAMMASOME;

ABDOMINAL DISTENSION; ADRENAL DISEASE; ADRENAL GLAND ENLARGEMENT; ALANINE AMINOTRANSFERASE BLOOD LEVEL; ANEMIA; ARTICLE; ASCITES; ASPARTATE AMINOTRANSFERASE BLOOD LEVEL; BILIRUBIN BLOOD LEVEL; BIRTH WEIGHT; CASE REPORT; COMPUTER ASSISTED TOMOGRAPHY; DIARRHEA; ENZYME ACTIVATION; FAILURE TO THRIVE; FEMALE; FEVER; GESTATIONAL AGE; HEMOPHAGOCYTIC SYNDROME; HEPATOMEGALY; HEPATOSPLENOMEGALY; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; HYPERBILIRUBINEMIA; HYPERTRANSAMINASEMIA; HYPERTRIGLYCERIDEMIA; INFANT; ITALIAN (CITIZEN); LACTATE DEHYDROGENASE BLOOD LEVEL; LIVER BIOPSY; LIVER FAILURE; MACROPHAGE; SPLENOMEGALY; THROMBOCYTOPENIA; VOMITING; WOLMAN DISEASE; COMPLICATION; FATALITY; LYMPHOHISTIOCYTOSIS, HEMOPHAGOCYTIC; METABOLISM;

BIOLOGICAL MARKERS; CHOLESTEROL ESTERS; FATAL OUTCOME; FEMALE; HUMANS; INFANT; INFLAMMASOMES; LYMPHOHISTIOCYTOSIS, HEMOPHAGOCYTIC; WOLMAN DISEASE;

EID: 84918830930     PISSN: 03406199     EISSN: 14321076     Source Type: Journal    
DOI: 10.1007/s00431-014-2338-y     Document Type: Article

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