Pathophysiology of brain dysfunction in hyperammonemic syndromes: The many faces of glutamine

Molecular Genetics and Metabolism

Volumn 113, Issue 1, 2014, Pages 113-117

  Butterworth, Roger F ^a  

^a UNIVERSITY OF MONTREAL   (Canada)

Author keywords

Alzheimer type 2 astrocytosis; Ammonia; Brain edema; Glutamine; Hepatic encephalopathy; Urea cycle enzymopathies

Indexed keywords

ALPHA KETOGLUTARAMATE; AMMONIA; GLUTAMATE AMMONIA LIGASE; GLUTAMINASE; GLUTAMINE; MITOCHONDRIAL ENZYME; NEUROTOXIN; UNCLASSIFIED DRUG; ALPHA-KETOGLUTAMIC ACID; GLUTAMATE TRANSPORTER; GLUTAMIC ACID DERIVATIVE;

ACUTE LIVER FAILURE; ARTICLE; BIOACCUMULATION; BRAIN DISEASE; BRAIN DYSFUNCTION; BRAIN EDEMA; DEAMINATION; DISEASE SEVERITY; HEPATIC ENCEPHALOPATHY; HUMAN; HYPERAMMONEMIA; INBORN ERROR OF METABOLISM; LIVER FAILURE; NEUROTRANSMISSION; NUCLEAR MAGNETIC RESONANCE SPECTROSCOPY; PATHOGENESIS; PATHOPHYSIOLOGY; PROTEIN INTAKE; PROTEIN SYNTHESIS; SKELETAL MUSCLE; TRANSAMINATION; UREA CYCLE ENZYMOPATHY; BRAIN DISEASES; COMPLICATION; METABOLISM; MITOCHONDRION; NERVE CELL; SYNDROME;

AMINO ACID TRANSPORT SYSTEM X-AG; BRAIN DISEASES; GLUTAMATES; GLUTAMINASE; GLUTAMINE; HUMANS; HYPERAMMONEMIA; MITOCHONDRIA; NEURONS; SYNDROME;

EID: 84908505093     PISSN: 10967192     EISSN: 10967206     Source Type: Journal    
DOI: 10.1016/j.ymgme.2014.06.003     Document Type: Article

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