Hermansky-pudlak syndrome complicated by pulmonary fibrosis: Radiologic-pathologic correlation and review of pulmonary complications

Journal of Clinical Imaging Science

Volumn 4, Issue 1, 2014, Pages 59-

  Kelil, Tatiana ^a   Shen, Jeanne ^a   O'Neill, Ailbhe ^b   Howard, Stephanie ^a  

^a BRIGHAM AND WOMEN S HOSPITAL   (United States)

^b DANA FARBER CANCER INSTITUTE   (United States)

Author keywords

Hermansky Pudlak syndrome; oculocutaneous hypopigmentation; platelet dysfunction; pulmonary fibrosis

Indexed keywords

ANTIBIOTIC AGENT; CREATININE;

ADULT; ANTIBIOTIC THERAPY; AUTOPSY; BLINDNESS; CASE REPORT; CORRELATIONAL STUDY; COUGHING; DISEASE COURSE; DISEASE SEVERITY; DYSPNEA; FEMALE; HEART RIGHT VENTRICLE FAILURE; HOSPITAL ADMISSION; HUMAN; HUMAN TISSUE; HYPERTRANSAMINASEMIA; HYPOXIA; INTENSIVE CARE; LUNG FIBROSIS; LUNG FUNCTION TEST; MULTIPLE ORGAN FAILURE; NONINVASIVE VENTILATION; OCULAR ALBINISM; OXYGEN THERAPY; PROGNOSIS; REVIEW; THORAX PAIN; THORAX RADIOGRAPHY; TOTAL LUNG CAPACITY;

EID: 84908460380     PISSN: None     EISSN: 21565597     Source Type: Journal    
DOI: 10.4103/2156-7514.143437     Document Type: Review

References (10)

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