Papillon-Lefèvre syndrome patient reveals species-dependent requirements for neutrophil defenses

Journal of Clinical Investigation

Volumn 124, Issue 10, 2014, Pages 4539-4548

  Sørensen, Ole E ^a   Clemmensen, Stine N ^b   Dahl, Sara L ^b   Østergaard, Ole ^c   Heegaard, Niels H ^c   Glenthøj, Andreas ^b   Nielsen, Finn Cilius ^d   Borregaard, Niels ^b  

^a LUND UNIVERSITY   (Sweden)

^b Rigshospitalet   (Denmark)

^c ODENSE UNIVERSITY HOSPITAL   (Denmark)

^d Mental Health Services CPH   (Denmark)

Author keywords

[No Author keywords available]

Indexed keywords

AZUROCIDIN; CATHELICIDIN; CATHELICIDIN ANTIMICROBIAL PEPTIDE LL 37; CATHELICIDIN HCAP 18; CATHEPSIN G; CHLORAMPHENICOL; CYSTEINE PROTEASE CATHEPSIN C; DEFENSIN; DIPEPTIDYL PEPTIDASE I; ELASTASE; IONOMYCIN; MYELOBLASTIN; REACTIVE OXYGEN METABOLITE; SERINE PROTEINASE; UNCLASSIFIED DRUG; ANTIMICROBIAL CATIONIC PEPTIDE; CAP18 LIPOPOLYSACCHARIDE-BINDING PROTEIN; PROTEOME;

ADULT; AGGRESSIVE PERIODONTITIS; ARTICLE; ATOPIC DERMATITIS; AZUROPHIL GRANULE; BACTERICIDAL ACTIVITY; BIOSYNTHESIS; BONE MARROW CELL; CASE REPORT; CELL FRACTIONATION; CELL GRANULE; CELL SELECTION; CELLULAR IMMUNITY; CONCENTRATION RESPONSE; CONTROLLED STUDY; ENZYME DEGRADATION; FEMALE; HOMOZYGOSITY; HUMAN; HUMAN CELL; IN VITRO STUDY; KLEBSIELLA PNEUMONIAE; MISSENSE MUTATION; NEUTROPHIL; NEUTROPHIL GRANULE; NONHUMAN; PAPILLON LEFEVRE SYNDROME; POLLEN ALLERGY; PROTEIN ANALYSIS; PROTEIN LOCALIZATION; SKIN ABSCESS; STAPHYLOCOCCUS AUREUS; STEM CELL; TONSILLECTOMY; TONSILLITIS; TOPICAL TREATMENT; TREATMENT RESPONSE; YOUNG ADULT; BONE MARROW; CELL SEPARATION; CYTOLOGY; FLOW CYTOMETRY; GENETICS; HOMOZYGOTE; IMMUNE SYSTEM; METABOLISM;

ADULT; ANTIMICROBIAL CATIONIC PEPTIDES; BONE MARROW; CATHEPSIN C; CELL SEPARATION; DEFENSINS; FEMALE; FLOW CYTOMETRY; HOMOZYGOTE; HUMANS; IMMUNE SYSTEM; IONOMYCIN; MUTATION, MISSENSE; NEUTROPHILS; PAPILLON-LEFEVRE DISEASE; PROTEOME; REACTIVE OXYGEN SPECIES; SERINE PROTEASES; SUBCELLULAR FRACTIONS;

EID: 84907486038     PISSN: 00219738     EISSN: 15588238     Source Type: Journal    
DOI: 10.1172/JCI76009     Document Type: Article

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