Primary pigmented nodular adrenocortical disease: The Original 4 cases revisited after 30 years for follow-up, new investigations, and molecular genetic findings

American Journal of Surgical Pathology

Volumn 38, Issue 9, 2014, Pages 1266-1273

  Carney, J Aidan ^a   Libé, Rossella ^b   Bertherat, Jérôme ^b   Young, William F ^a  

^a MAYO CLINIC   (United States)

^b Service d'Endocrinologie Hô Pital Cochin   (France)

Author keywords

adrenal; Cushing syndrome; genetics; micronodules; PRKAR1A mutation

Indexed keywords

BIOLOGICAL MARKER; CYCLIC AMP DEPENDENT PROTEIN KINASE REGULATORY SUBUNIT IALPHA; DEXAMETHASONE; DIAGNOSTIC AGENT; HYDROCORTISONE; PRKAR1A PROTEIN, HUMAN;

ADOLESCENT; ADRENAL CORTEX DISEASE; ADRENALECTOMY; ARTICLE; CARNEY COMPLEX; CHILD; CUSHING SYNDROME; FEMALE; FOLLOW UP; GENE DELETION; GENETIC PREDISPOSITION; GENETICS; HUMAN; IMMUNOHISTOCHEMISTRY; MALE; METABOLISM; PATHOLOGY; PHENOTYPE; POLYMERASE CHAIN REACTION; PREDICTIVE VALUE; TIME; TREATMENT OUTCOME; URINE; YOUNG ADULT;

ADOLESCENT; ADRENAL CORTEX DISEASES; ADRENALECTOMY; BIOLOGICAL MARKERS; CARNEY COMPLEX; CHILD; CUSHING SYNDROME; CYCLIC AMP-DEPENDENT PROTEIN KINASE RIALPHA SUBUNIT; DEXAMETHASONE; FEMALE; FOLLOW-UP STUDIES; GENE DELETION; GENETIC PREDISPOSITION TO DISEASE; HUMANS; HYDROCORTISONE; IMMUNOHISTOCHEMISTRY; MALE; PHENOTYPE; POLYMERASE CHAIN REACTION; PREDICTIVE VALUE OF TESTS; TIME FACTORS; TREATMENT OUTCOME; YOUNG ADULT;

EID: 84906794275     PISSN: 01475185     EISSN: 15320979     Source Type: Journal    
DOI: 10.1097/PAS.0000000000000220     Document Type: Article

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