Absence of lipofuscin in motor neurons of SOD1-linked ALS mice

Proceedings of the National Academy of Sciences of the United States of America

Volumn 111, Issue 30, 2014, Pages 11055-11060

  Bandyopadhyay, Urmi ^a   Nagy, Maria ^a   Fenton, Wayne A ^a   Horwich, Arthur L ^a  

^a YALE UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CHLOROQUINE; COPPER ZINC SUPEROXIDE DISMUTASE; HYDROXYMETHYLGLUTARYL COENZYME A REDUCTASE KINASE; LIPOFUSCIN; MAMMALIAN TARGET OF RAPAMYCIN COMPLEX 1; MICROTUBULE ASSOCIATED PROTEIN 1; PROTEIN P62; UBIQUITINATED PROTEIN;

ANIMAL CELL; ANIMAL EXPERIMENT; ARTICLE; AUTOFLUORESCENCE; AUTOPHAGOSOME; AUTOPHAGY; BLOOD BRAIN BARRIER; CELL METABOLISM; CONTROLLED STUDY; MOTONEURON; MOUSE; NONHUMAN; PERIKARYON; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN HYDROLYSIS; PROTEIN PHOSPHORYLATION; SPINAL CORD TRANSSECTION; SPINAL CORD VENTRAL HORN;

ADAPTOR PROTEINS, SIGNAL TRANSDUCING; AMINO ACID SUBSTITUTION; AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; AUTOPHAGY; HEAT-SHOCK PROTEINS; HUMANS; LIPOFUSCIN; LYSOSOMES; MICE; MICE, TRANSGENIC; MICROTUBULE-ASSOCIATED PROTEINS; MOTOR NEURONS; MULTIPROTEIN COMPLEXES; MUTATION, MISSENSE; PROTEIN-SERINE-THREONINE KINASES; SUPEROXIDE DISMUTASE; TOR SERINE-THREONINE KINASES;

EID: 84905040018     PISSN: 00278424     EISSN: 10916490     Source Type: Journal    
DOI: 10.1073/pnas.1409314111     Document Type: Article

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