Rapid-onset obesity with hypothalamic dysfunction, hypoventilation, and autonomic dysregulation: Review and update

Current Opinion in Pediatrics

Volumn 26, Issue 4, 2014, Pages 487-492

  Patwari, Pallavi P ^a   Wolfe, Lisa F ^a  

^a NORTHWESTERN UNIVERSITY   (United States)

Author keywords

genetic; hypothalamic dysfunction; hypoventilation; obesity; paraneoplastic

Indexed keywords

HOMEODOMAIN PROTEIN; PAIRED LIKE HOMEOBOX 2B; UNCLASSIFIED DRUG; AGENTS INTERACTING WITH TRANSMITTER, HORMONE OR DRUG RECEPTORS; NEUROPEPTIDE; OREXIN RECEPTOR; OREXINS; SIGNAL PEPTIDE;

AUTONOMIC DYSFUNCTION; AUTONOMIC NERVOUS SYSTEM DYSREGULATION; AUTONOMIC NEUROPATHY; CONGENITAL CENTRAL HYPOVENTILATION SYNDROME; DISEASE ASSOCIATION; DNA BINDING; GENE MUTATION; GENETIC SCREENING; HUMAN; HYPOTHALAMUS DISEASE; HYPOVENTILATION; OBESITY; PATHOPHYSIOLOGY; PRIORITY JOURNAL; RAPID ONSET OBESITY WITH HYPOTHALAMIC DYSFUNCTION HYPOVENTILATION AND AUTONOMIC DYSREGULATION; REVIEW; CENTRAL SLEEP APNEA SYNDROME; GENETIC VARIABILITY; GENETICS; METABOLISM; PHENOTYPE; RARE DISEASE;

AUTONOMIC NERVOUS SYSTEM DISEASES; GENETIC VARIATION; HUMANS; HYPOVENTILATION; INTRACELLULAR SIGNALING PEPTIDES AND PROTEINS; NEUROPEPTIDES; NEUROTRANSMITTER AGENTS; OBESITY; OREXIN RECEPTORS; PHENOTYPE; RARE DISEASES; SLEEP APNEA, CENTRAL;

EID: 84904462370     PISSN: 10408703     EISSN: 1531698X     Source Type: Journal    
DOI: 10.1097/MOP.0000000000000118     Document Type: Review

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