Clinical manifestations of autosomal recessive polycystic kidney disease (ARPKD): kidney-related and non-kidney-related phenotypes

Pediatric Nephrology

Volumn 29, Issue 10, 2014, Pages 1915-1925

  Büscher, Rainer ^a   Büscher, Anja K ^a   Weber, Stefanie ^a   Mohr, Julia ^b   Hegen, Bianca ^a   Vester, Udo ^a   Hoyer, Peter F ^a  

^a UNIVERSITY OF DUISBURG ESSEN   (Germany)

^b HELIOS KLINIKUM KREFELD   (Germany)

Author keywords

ARPKD; Caroli s syndrome; Children; Extrarenal manifestation; Hepatic fibrosis; Portal hypertension

Indexed keywords

ANGIOTENSIN RECEPTOR ANTAGONIST; ANTIBIOTIC AGENT; BETA ADRENERGIC RECEPTOR BLOCKING AGENT; CALCIUM CHANNEL BLOCKING AGENT; COTRIMOXAZOLE; DIPEPTIDYL CARBOXYPEPTIDASE INHIBITOR; FIBROCYSTIN; OCTREOTIDE; PROPRANOLOL; RAPAMYCIN; TRIMETHOPRIM; URSODEOXYCHOLIC ACID;

ANTIBIOTIC THERAPY; ARTICLE; DISEASE ASSOCIATION; DRUG EFFICACY; ESOPHAGUS VARICES; ESOPHAGUS VARICES BLEEDING; HEPATOBILIARY DISEASE; HUMAN; HYPERTENSION; KIDNEY DISEASE; KIDNEY FUNCTION; KIDNEY POLYCYSTIC DISEASE; KIDNEY TRANSPLANTATION; LIVER DISEASE; LIVER FIBROSIS; LIVER TRANSPLANTATION; LUNG HYPOPLASIA; NONHUMAN; PANCREAS CYST; PHENOTYPE; PORTAL HYPERTENSION; PRIORITY JOURNAL; RISK FACTOR; SCLEROTHERAPY; SYMPTOM; COMPLICATION; PATHOLOGY;

HUMANS; PHENOTYPE; POLYCYSTIC KIDNEY, AUTOSOMAL RECESSIVE;

EID: 84903570761     PISSN: 0931041X     EISSN: 1432198X     Source Type: Journal    
DOI: 10.1007/s00467-013-2634-1     Document Type: Article

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