Pulmonary Vein stenosis with Down syndrome: A rare and frequently fatal cause of pulmonary hypertension in infants and children

Congenital Heart Disease

Volumn 9, Issue 3, 2014, Pages

  Gowda, Srinath ^a   Bhat, Deepti ^a   Feng, Zhuang ^a   Chang, Chung Ho ^a   Ross, Robert D ^a  

^a CHILDREN'S HOSPITAL OF MICHIGAN   (United States)

Author keywords

Catheterization; Down syndrome; Pulmonary hypertension; Pulmonary vein stenosis

Indexed keywords

BOSENTAN; MILRINONE; SILDENAFIL; ANTIHYPERTENSIVE AGENT;

ARTICLE; ARTIFICIAL VENTILATION; ASPIRATION PNEUMONIA; CARDIOPULMONARY ARREST; CARDIOVASCULAR MORTALITY; CASE REPORT; DISEASE COURSE; DISEASE SEVERITY; DOPPLER ECHOGRAPHY; DOWN SYNDROME; ECHOCARDIOGRAPHY; FEMALE; FENESTRATION; FOLLOW UP; HEART ATRIUM SEPTUM DEFECT; HEART CATHETERIZATION; HEART FAILURE; HEART HEMODYNAMICS; HEART LEFT ATRIUM; HEART RIGHT VENTRICLE PRESSURE; HIGH RISK INFANT; HISTOPATHOLOGY; HOSPITAL ADMISSION; HOSPITAL DISCHARGE; HUMAN; HYPOXIA; INFANT; INTENSIVE CARE; LOBECTOMY; LUNG ARTERY PRESSURE; LUNG RESECTION; LUNG VASCULAR RESISTANCE; LUNG WEDGE PRESSURE; MALE; MITRAL VALVE PROSTHESIS; MITRAL VALVE REGURGITATION; OXYGEN THERAPY; PALLIATIVE THERAPY; PERCUTANEOUS TRANSLUMINAL ANGIOPLASTY; PRIORITY JOURNAL; PULMONARY HYPERTENSION; PULMONARY VEIN; PULMONARY VEIN MALFORMATION; PULMONARY VEIN OBSTRUCTION; RARE DISEASE; RESPIRATORY DISTRESS; TRACHEOSTOMY; AGE; ARTERIAL PRESSURE; COMPLICATION; FATALITY; HYPERTENSION, PULMONARY; LUNG CIRCULATION; PATHOPHYSIOLOGY; PULMONARY ARTERY; PULMONARY VENO-OCCLUSIVE DISEASE; RISK FACTOR; STENOSIS, OCCLUSION AND OBSTRUCTION; TIME; TREATMENT OUTCOME; VASCULAR SURGERY;

AGE FACTORS; ANGIOPLASTY, BALLOON; ANTIHYPERTENSIVE AGENTS; ARTERIAL PRESSURE; CONSTRICTION, PATHOLOGIC; DISEASE PROGRESSION; DOWN SYNDROME; FATAL OUTCOME; FEMALE; HUMANS; HYPERTENSION, PULMONARY; INFANT; MALE; PULMONARY ARTERY; PULMONARY CIRCULATION; PULMONARY VEINS; PULMONARY VENO-OCCLUSIVE DISEASE; RISK FACTORS; TIME FACTORS; TREATMENT OUTCOME; VASCULAR SURGICAL PROCEDURES;

EID: 84902536567     PISSN: 1747079X     EISSN: 17470803     Source Type: Journal    
DOI: 10.1111/chd.12088     Document Type: Article

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