Atrio-ventricular block requiring pacemaker in patients with late onset Pompe disease

Neuromuscular Disorders

Volumn 24, Issue 7, 2014, Pages 648-650

  Sacconi, Sabrina ^a   Wahbi, Karim ^b,c   Theodore, Guillaume ^d   Garcia, Jérémy ^a   Salviati, Leonardo ^e,f   Bouhour, Françoise ^g   Vial, Christophe ^g   Duboc, Denis ^b   Laforêt, Pascal ^c   Desnuelle, Claude ^a  

^a CENTRE HOSPITALIER UNIVERSITAIRE DE NICE   (France)

^b Cardiology Department Cochin Hospital APHP ^*  (France)

^c PITIÉ SALPÊTRIÈRE HOSPITAL   (France)

^d PASTEUR HOSPITAL   (France)

^e UNIVERSITY OF PADOVA   (Italy)

^f Pediatric Research Institute   (Italy)

^g Institute for Cognitive Sciences   (France)

Author keywords

Atrioventricular block; Cardiomyopathy; Holter EKG; Late onset Pompe disease; Pacemaker; Pompe disease

Indexed keywords

ALPHA GLUCOSIDASE;

ADULT; ARTICLE; ASYMPTOMATIC DISEASE; ATRIOVENTRICULAR BLOCK; CLINICAL FEATURE; COHORT ANALYSIS; DISEASE SEVERITY; ELECTROCARDIOGRAM; ELECTROCARDIOGRAPHY; ENZYME REPLACEMENT; FEMALE; GLYCOGEN STORAGE DISEASE TYPE 2; HUMAN; IMPLANTED HEART PACEMAKER; LATE ONSET POMPE DISEASE; MAJOR CLINICAL STUDY; MALE; MIDDLE AGED; MUSCLE WEAKNESS; PRIORITY JOURNAL; RESPIRATORY FAILURE; RETROSPECTIVE STUDY; ARTIFICIAL HEART PACEMAKER; CASE REPORT; ECHOCARDIOGRAPHY; FATALITY; FRANCE; GLYCOGEN STORAGE DISEASE TYPE II; HEART; ONSET AGE; PATHOPHYSIOLOGY;

ADULT; AGE OF ONSET; ATRIOVENTRICULAR BLOCK; ECHOCARDIOGRAPHY; FATAL OUTCOME; FEMALE; FRANCE; GLYCOGEN STORAGE DISEASE TYPE II; HEART; HUMANS; MALE; MIDDLE AGED; PACEMAKER, ARTIFICIAL; RETROSPECTIVE STUDIES;

EID: 84901947673     PISSN: 09608966     EISSN: 18732364     Source Type: Journal    
DOI: 10.1016/j.nmd.2014.04.005     Document Type: Article

References (11)

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