Progressive hepatic mitochondrial dysfunction in premanifest Huntington's disease

Movement Disorders

Volumn 29, Issue 6, 2014, Pages 831-834

  Hoffmann, Rainer ^a   Stüwe, Sven H ^a   Goetze, Oliver ^b   Banasch, Matthias ^a   Klotz, Peter ^a   Lukas, Carsten ^a   Tegenthoff, Martin ^c   Beste, Christian ^d   Orth, Michael ^e   Saft, Carsten ^a  

^a RUHR UNIVERSITY BOCHUM   (Germany)

^b UNIVERSITY HOSPITAL WÜRZBURG   (Germany)

^c RUHR UNIVERSITY BOCHUM   (Germany)

^d UNIVERSITY HOSPITAL CARL GUSTAV CARUS   (Germany)

^e UNIVERSITY OF ULM   (Germany)

Author keywords

Liver; Methionine; Mitochondria; Premanifest Huntington's disease

Indexed keywords

METHIONINE; METHIONINE C 13; RADIOPHARMACEUTICAL AGENT; UNCLASSIFIED DRUG; HTT PROTEIN, HUMAN; NERVE PROTEIN;

ADULT; ARTICLE; BREATH ANALYSIS; CAG REPEAT; CLINICAL ARTICLE; DISORDERS OF MITOCHONDRIAL FUNCTIONS; FEMALE; FOLLOW UP; FUNCTIONAL STATUS; HUMAN; HUNTINGTON CHOREA; IN VIVO STUDY; LIVER DISEASE; LONGITUDINAL STUDY; MALE; METHIONINE C 13 BREATH TEST; MOTOR PERFORMANCE; PILOT STUDY; PRIORITY JOURNAL; PROGRESSIVE HEPATIC MITOCHONDRIAL DYSFUNCTION; STROOP TEST; STUDENT T TEST; UNIFIED HUNTINGTON DISEASE RATING SCALE; COMPLICATION; DISEASE COURSE; GENETICS; LIVER DISEASES; MIDDLE AGED; MITOCHONDRIAL DISEASES; MITOCHONDRION; PATHOLOGY; STATISTICS; TRINUCLEOTIDE REPEAT; YOUNG ADULT;

ADULT; DISEASE PROGRESSION; FEMALE; FOLLOW-UP STUDIES; HUMANS; HUNTINGTON DISEASE; LIVER DISEASES; MALE; MIDDLE AGED; MITOCHONDRIA; MITOCHONDRIAL DISEASES; NERVE TISSUE PROTEINS; STATISTICS AS TOPIC; TRINUCLEOTIDE REPEATS; YOUNG ADULT;

EID: 84899939410     PISSN: 08853185     EISSN: 15318257     Source Type: Journal    
DOI: 10.1002/mds.25862     Document Type: Article

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