Arrhythmogenic right ventricular cardiomyopathy in a 20-year-old woman with systemic sclerosis

Internal Medicine

Volumn 53, Issue 9, 2014, Pages 973-977

  Dohi, Kaoru ^a   Nakamori, Shiro ^a   Kurita, Tairo ^a   Omoto, Youichi ^a   Ishida, Masaki ^a   Nakamura, Mashio ^a   Imanaka Yoshida, Kyoko ^a   Sakuma, Hajime ^a   Mizutani, Hitoshi ^a   Ito, Masaaki ^a  

^a MIE UNIVERSITY GRADUATE SCHOOL OF MEDICINE   (Japan)

Author keywords

Arrhythmogenic right ventricular cardiomyopathy; Sudden death; Systemic sclerosis

Indexed keywords

ADULT; ARTICLE; ATROPHY; CARDIOVASCULAR MAGNETIC RESONANCE; CASE REPORT; COMPUTER ASSISTED TOMOGRAPHY; DISEASE ASSOCIATION; DYSKINESIA; DYSPNEA; ELECTROCARDIOGRAPHY; FEMALE; FIBROSING ALVEOLITIS; HEART CATHETERIZATION; HEART MUSCLE ATROPHY; HEART MUSCLE BIOPSY; HEART PALPITATION; HEART RIGHT BUNDLE BRANCH BLOCK; HEART RIGHT VENTRICLE DYSPLASIA; HEART VENTRICLE ANEURYSM; HEART VENTRICLE TACHYCARDIA; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; IMPLANTABLE CARDIOVERTER DEFIBRILLATOR; NUCLEAR MAGNETIC RESONANCE IMAGING; SYSTEMIC SCLEROSIS; THORAX PAIN; THORAX RADIOGRAPHY; TRICUSPID VALVE REGURGITATION; TWO DIMENSIONAL ECHOCARDIOGRAPHY; YOUNG ADULT; ARRHYTHMOGENIC RIGHT VENTRICULAR DYSPLASIA; BIOPSY; COMPLICATION; DIFFERENTIAL DIAGNOSIS; FATALITY; HEART RIGHT VENTRICLE FUNCTION; HEART VENTRICLE; PATHOLOGY; PATHOPHYSIOLOGY; PROCEDURES; SCLERODERMA, SYSTEMIC;

ARRHYTHMOGENIC RIGHT VENTRICULAR DYSPLASIA; BIOPSY; CARDIAC CATHETERIZATION; DIAGNOSIS, DIFFERENTIAL; ELECTROCARDIOGRAPHY; FATAL OUTCOME; FEMALE; HEART VENTRICLES; HUMANS; MAGNETIC RESONANCE IMAGING; MAGNETIC RESONANCE IMAGING, CINE; SCLERODERMA, SYSTEMIC; VENTRICULAR FUNCTION, RIGHT; YOUNG ADULT;

EID: 84899763704     PISSN: 09182918     EISSN: 13497235     Source Type: Journal    
DOI: 10.2169/internalmedicine.53.1977     Document Type: Article

References (10)

1. Marcus FI, McKenna WJ, Sherrill D, et al. Diagnosis of arrhythmogenic right ventricular cardiomyopathy/dysplasia: proposed modification of the task force criteria. Circulation 121: 1533-1541, 2010.
2. Ferri C, Valentini G, Cozzi F, et al. Systemic sclerosis: demographic, clinical, and serologic features and survival in 1,012 Italian patients. Medicine 81: 139-153, 2002.
3. Steen VD, Medsger TA Jr. Severe organ involvement in systemic sclerosis with diffuse scleroderma. Arthritis Rheum 43: 2437-2444, 2000.
4. Kahan A, Coghlan G, McLaughlin V. Cardiac complications of systemic sclerosis. Rheumatology (Oxford) 48 (Suppl 3): iii45-iii 48, 2009.
5. Hachulla AL, Launay D, Gaxotte V, et al. Cardiac magnetic resonance imaging in systemic sclerosis: a cross-sectional observational study of 52 patients. Ann Rheum Dis 68: 1878-1884, 2009.
6. Corrado D, Fontaine G, Marcus FI, et al. Arrhythmogenic right ventricular dysplasia/cardiomyopathy: need for an international registry. Study Group on Arrhythmogenic Right Ventricular Dysplasia/ Cardiomyopathy of the Working Groups on Myocardial and Pericardial Disease and Arrhythmias of the European Society of Cardiology and of the Scientific Council on Cardiomyopathies of the World Heart Federation. Circulation 101: E101-E106, 2000.
7. Sen-Chowdhry S, Lowe MD, Sporton SC, McKenna WJ. Arrhythmogenic right ventricular cardiomyopathy: clinical presentation, diagnosis, and management. Am J Med 117: 685-695, 2004.
8. Arai S, Kurasawa K, Maezawa R, Hanaoka R, Fukuda T. Systemic sclerosis complicated by arrhythmogenic right ventricular dysplasia that was misinterpreted as pulmonary arterial hypertension. Mod Rheumatol 22: 152-157, 2012.
9. Giusti B, Margheri F, Rossi L, et al. Desmoglein-2-integrin Beta-8 interaction regulates actin assembly in endothelial cells: deregulation in systemic sclerosis. PLoS One 8: e68117, 2013.
10. Jain A, Tandri H, Calkins H, Bluemke DA. Role of cardiovascular magnetic resonance imaging in arrhythmogenic right ventricular dysplasia. J Cardiovasc Magn Reson 10: 32, 2008.