-
2
-
-
0025803107
-
Cystic fibrosis. 6. Gastrointestinal and nutritional aspects
-
H. Kopelman Cystic fibrosis. 6. Gastrointestinal and nutritional aspects Thorax 46 1991 261 267
-
(1991)
Thorax
, vol.46
, pp. 261-267
-
-
Kopelman, H.1
-
3
-
-
33744762758
-
Review of the abdominal manifestations of cystic fibrosis in the adult patient
-
M.B. Robertson, K.A. Choe, and P.M. Joseph Review of the abdominal manifestations of cystic fibrosis in the adult patient Radiographics 26 2006 679 690
-
(2006)
Radiographics
, vol.26
, pp. 679-690
-
-
Robertson, M.B.1
Choe, K.A.2
Joseph, P.M.3
-
4
-
-
0016417460
-
Pathology of cystic fibrosis review of the literature and comparison with 146 autopsied cases
-
E.H. Oppenheimer, and J.R. Esterly Pathology of cystic fibrosis review of the literature and comparison with 146 autopsied cases Perspect Pediatr Pathol 2 1975 241 278
-
(1975)
Perspect Pediatr Pathol
, vol.2
, pp. 241-278
-
-
Oppenheimer, E.H.1
Esterly, J.R.2
-
5
-
-
0032962320
-
Pathophysiology of gene-targeted mouse models for cystic fibrosis
-
B.R. Grubb, and R.C. Boucher Pathophysiology of gene-targeted mouse models for cystic fibrosis Physiol Rev 79 1999 S193 S214
-
(1999)
Physiol Rev
, vol.79
-
-
Grubb, B.R.1
Boucher, R.C.2
-
6
-
-
79958134728
-
Mouse models of cystic fibrosis: Phenotypic analysis and research applications
-
M. Wilke, R.M. Buijs-Offerman, J. Aarbiou, W.H. Colledge, D.N. Sheppard, L. Touqui, A. Bot, H. Jorna, H.R. de Jonge, and B.J. Scholte Mouse models of cystic fibrosis: phenotypic analysis and research applications J Cyst Fibros 10 Suppl 2 2011 S152 S171
-
(2011)
J Cyst Fibros
, vol.10
, Issue.SUPPL. 2
-
-
Wilke, M.1
Buijs-Offerman, R.M.2
Aarbiou, J.3
Colledge, W.H.4
Sheppard, D.N.5
Touqui, L.6
Bot, A.7
Jorna, H.8
De Jonge, H.R.9
Scholte, B.J.10
-
7
-
-
41849148289
-
Production of CFTR-null and CFTR-DeltaF508 heterozygous pigs by adeno-associated virus-mediated gene targeting and somatic cell nuclear transfer
-
C.S. Rogers, Y. Hao, T. Rokhlina, M. Samuel, D.A. Stoltz, Y. Li, E. Petroff, D.W. Vermeer, A.C. Kabel, Z. Yan, L. Spate, D. Wax, C.N. Murphy, A. Rieke, K. Whitworth, M.L. Linville, S.W. Korte, J.F. Engelhardt, M.J. Welsh, and R.S. Prather Production of CFTR-null and CFTR-DeltaF508 heterozygous pigs by adeno-associated virus-mediated gene targeting and somatic cell nuclear transfer J Clin Invest 118 2008 1571 1577
-
(2008)
J Clin Invest
, vol.118
, pp. 1571-1577
-
-
Rogers, C.S.1
Hao, Y.2
Rokhlina, T.3
Samuel, M.4
Stoltz, D.A.5
Li, Y.6
Petroff, E.7
Vermeer, D.W.8
Kabel, A.C.9
Yan, Z.10
Spate, L.11
Wax, D.12
Murphy, C.N.13
Rieke, A.14
Whitworth, K.15
Linville, M.L.16
Korte, S.W.17
Engelhardt, J.F.18
Welsh, M.J.19
Prather, R.S.20
more..
-
8
-
-
41849102053
-
Adeno-associated virus-targeted disruption of the CFTR gene in cloned ferrets
-
X. Sun, Z. Yan, Y. Yi, Z. Li, D. Lei, C.S. Rogers, J. Chen, Y. Zhang, M.J. Welsh, G.H. Leno, and J.F. Engelhardt Adeno-associated virus-targeted disruption of the CFTR gene in cloned ferrets J Clin Invest 118 2008 1578 1583
-
(2008)
J Clin Invest
, vol.118
, pp. 1578-1583
-
-
Sun, X.1
Yan, Z.2
Yi, Y.3
Li, Z.4
Lei, D.5
Rogers, C.S.6
Chen, J.7
Zhang, Y.8
Welsh, M.J.9
Leno, G.H.10
Engelhardt, J.F.11
-
9
-
-
80053368675
-
New animal models of cystic fibrosis: What are they teaching us?
-
N.W. Keiser, and J.F. Engelhardt New animal models of cystic fibrosis: what are they teaching us? Curr Opin Pulm Med 17 2011 478 483
-
(2011)
Curr Opin Pulm Med
, vol.17
, pp. 478-483
-
-
Keiser, N.W.1
Engelhardt, J.F.2
-
10
-
-
80052538896
-
Comparative biology of cystic fibrosis animal models
-
J.T. Fisher, Y. Zhang, and J.F. Engelhardt Comparative biology of cystic fibrosis animal models Methods Mol Biol 742 2011 311 334
-
(2011)
Methods Mol Biol
, vol.742
, pp. 311-334
-
-
Fisher, J.T.1
Zhang, Y.2
Engelhardt, J.F.3
-
11
-
-
77749237132
-
Pathology of gastrointestinal organs in a porcine model of cystic fibrosis
-
D.K. Meyerholz, D.A. Stoltz, A.A. Pezzulo, and M.J. Welsh Pathology of gastrointestinal organs in a porcine model of cystic fibrosis Am J Pathol 176 2010 1377 1389
-
(2010)
Am J Pathol
, vol.176
, pp. 1377-1389
-
-
Meyerholz, D.K.1
Stoltz, D.A.2
Pezzulo, A.A.3
Welsh, M.J.4
-
12
-
-
77956379893
-
Disease phenotype of a ferret CFTR-knockout model of cystic fibrosis
-
X. Sun, H. Sui, J.T. Fisher, Z. Yan, X. Liu, H.J. Cho, N.S. Joo, Y. Zhang, W. Zhou, Y. Yi, J.M. Kinyon, D.C. Lei-Butters, M.A. Griffin, P. Naumann, M. Luo, J. Ascher, K. Wang, T. Frana, J.J. Wine, D.K. Meyerholz, and J.F. Engelhardt Disease phenotype of a ferret CFTR-knockout model of cystic fibrosis J Clin Invest 120 2010 3149 3160
-
(2010)
J Clin Invest
, vol.120
, pp. 3149-3160
-
-
Sun, X.1
Sui, H.2
Fisher, J.T.3
Yan, Z.4
Liu, X.5
Cho, H.J.6
Joo, N.S.7
Zhang, Y.8
Zhou, W.9
Yi, Y.10
Kinyon, J.M.11
Lei-Butters, D.C.12
Griffin, M.A.13
Naumann, P.14
Luo, M.15
Ascher, J.16
Wang, K.17
Frana, T.18
Wine, J.J.19
Meyerholz, D.K.20
Engelhardt, J.F.21
more..
-
13
-
-
84867166324
-
Abnormal endocrine pancreas function at birth in cystic fibrosis ferrets
-
A.K. Olivier, Y. Yi, X. Sun, H. Sui, B. Liang, S. Hu, W. Xie, J.T. Fisher, N.W. Keiser, D. Lei, W. Zhou, Z. Yan, G. Li, T.I. Evans, D.K. Meyerholz, K. Wang, Z.A. Stewart, A.W. Norris, and J.F. Engelhardt Abnormal endocrine pancreas function at birth in cystic fibrosis ferrets J Clin Invest 122 2012 3755 3768
-
(2012)
J Clin Invest
, vol.122
, pp. 3755-3768
-
-
Olivier, A.K.1
Yi, Y.2
Sun, X.3
Sui, H.4
Liang, B.5
Hu, S.6
Xie, W.7
Fisher, J.T.8
Keiser, N.W.9
Lei, D.10
Zhou, W.11
Yan, Z.12
Li, G.13
Evans, T.I.14
Meyerholz, D.K.15
Wang, K.16
Stewart, Z.A.17
Norris, A.W.18
Engelhardt, J.F.19
-
14
-
-
84899502263
-
Lung phenotype of juvenile and adult CFTR-knockout ferrets
-
(In Press)
-
X. Sun, A.K. Olivier, B. Liang, Y. Yi, H. Sui, T.I. Evans, Y. Zhang, W. Zhou, S.R. Tyler, J.T. Fisher, N.W. Keiser, X. Liu, Z. Yan, Y. Song, J.A. Goeken, J.M. Kinyon, D. Fligg, X. Wang, W. Xie, T.J. Lynch, P.M. Kaminsky, Z.A. Stewart, R.M. Pope, T. Frana, D.K. Meyerholz, K. Parekh, and J.F. Engelhardt Lung phenotype of juvenile and adult CFTR-knockout ferrets Am J Respir Cell Mol Biol 2013 (In Press)
-
(2013)
Am J Respir Cell Mol Biol
-
-
Sun, X.1
Olivier, A.K.2
Liang, B.3
Yi, Y.4
Sui, H.5
Evans, T.I.6
Zhang, Y.7
Zhou, W.8
Tyler, S.R.9
Fisher, J.T.10
Keiser, N.W.11
Liu, X.12
Yan, Z.13
Song, Y.14
Goeken, J.A.15
Kinyon, J.M.16
Fligg, D.17
Wang, X.18
Xie, W.19
Lynch, T.J.20
Kaminsky, P.M.21
Stewart, Z.A.22
Pope, R.M.23
Frana, T.24
Meyerholz, D.K.25
Parekh, K.26
Engelhardt, J.F.27
more..
-
15
-
-
0003531306
-
-
P.J. Quinn, M.E. Carter, B.K. Markey, G.R. Carter, Wolfe London
-
P.J. Quinn Clinical veterinary microbiology P.J. Quinn, M.E. Carter, B.K. Markey, G.R. Carter, 1994 Wolfe London 648
-
(1994)
Clinical Veterinary Microbiology
, pp. 648
-
-
Quinn, P.J.1
-
16
-
-
80052250369
-
Improved performance of bacterium and yeast identification by a commercial matrix-assisted laser desorption ionization-time of flight mass spectrometry system in the clinical microbiology laboratory
-
J. Haigh, A. Degun, M. Eydmann, M. Millar, and M. Wilks Improved performance of bacterium and yeast identification by a commercial matrix-assisted laser desorption ionization-time of flight mass spectrometry system in the clinical microbiology laboratory J Clin Microbiol 49 2011 3441
-
(2011)
J Clin Microbiol
, vol.49
, pp. 3441
-
-
Haigh, J.1
Degun, A.2
Eydmann, M.3
Millar, M.4
Wilks, M.5
-
17
-
-
2442510059
-
Improved extraction of PCR-quality community DNA from digesta and fecal samples
-
Z. Yu, and M. Morrison Improved extraction of PCR-quality community DNA from digesta and fecal samples Biotechniques 36 2004 808 812
-
(2004)
Biotechniques
, vol.36
, pp. 808-812
-
-
Yu, Z.1
Morrison, M.2
-
18
-
-
84899554284
-
Escherichia coli dysbiosis correlates with gastrointestinal dysfunction in children with cystic fibrosis
-
L.R. Hoffman, C.E. Pope, H.S. Hayden, S. Heltshe, R. Levy, S. McNamara, M.A. Jacobs, L. Rohmer, M. Radey, B.W. Ramsey, M.J. Brittnacher, E. Borenstein, and S.I. Miller Escherichia coli dysbiosis correlates with gastrointestinal dysfunction in children with cystic fibrosis Clin Infect Dis 2013
-
(2013)
Clin Infect Dis
-
-
Hoffman, L.R.1
Pope, C.E.2
Hayden, H.S.3
Heltshe, S.4
Levy, R.5
McNamara, S.6
Jacobs, M.A.7
Rohmer, L.8
Radey, M.9
Ramsey, B.W.10
Brittnacher, M.J.11
Borenstein, E.12
Miller, S.I.13
-
19
-
-
84864440400
-
Metagenomic microbial community profiling using unique clade-specific marker genes
-
N. Segata, L. Waldron, A. Ballarini, V. Narasimhan, O. Jousson, and C. Huttenhower Metagenomic microbial community profiling using unique clade-specific marker genes Nat Methods 9 2012 811 814
-
(2012)
Nat Methods
, vol.9
, pp. 811-814
-
-
Segata, N.1
Waldron, L.2
Ballarini, A.3
Narasimhan, V.4
Jousson, O.5
Huttenhower, C.6
-
20
-
-
21444443190
-
Pancreatic exocrine function in patients with cystic fibrosis
-
S.S. Baker, D. Borowitz, and R.D. Baker Pancreatic exocrine function in patients with cystic fibrosis Curr Gastroenterol Rep 7 2005 227 233
-
(2005)
Curr Gastroenterol Rep
, vol.7
, pp. 227-233
-
-
Baker, S.S.1
Borowitz, D.2
Baker, R.D.3
-
22
-
-
77958152154
-
Update on cystic fibrosis-related diabetes
-
A.A. Stecenko, and A. Moran Update on cystic fibrosis-related diabetes Curr Opin Pulm Med 16 2010 611 615
-
(2010)
Curr Opin Pulm Med
, vol.16
, pp. 611-615
-
-
Stecenko, A.A.1
Moran, A.2
-
23
-
-
0034109607
-
Genotype and phenotype in cystic fibrosis
-
J. Zielenski Genotype and phenotype in cystic fibrosis Respiration 67 2000 117 133
-
(2000)
Respiration
, vol.67
, pp. 117-133
-
-
Zielenski, J.1
-
24
-
-
0032753456
-
Natural history of liver disease in cystic fibrosis
-
A. Lindblad, H. Glaumann, and B. Strandvik Natural history of liver disease in cystic fibrosis Hepatology 30 1999 1151 1158
-
(1999)
Hepatology
, vol.30
, pp. 1151-1158
-
-
Lindblad, A.1
Glaumann, H.2
Strandvik, B.3
-
25
-
-
67651099218
-
Hepatobiliary disease in patients with cystic fibrosis
-
K. Moyer, and W. Balistreri Hepatobiliary disease in patients with cystic fibrosis Curr Opin Gastroenterol 25 2009 272 278
-
(2009)
Curr Opin Gastroenterol
, vol.25
, pp. 272-278
-
-
Moyer, K.1
Balistreri, W.2
-
26
-
-
0022613164
-
Fatal hepatic necrosis after shock
-
H. Irie, and W. Mori Fatal hepatic necrosis after shock Acta Pathol Jpn 36 1986 363 374
-
(1986)
Acta Pathol Jpn
, vol.36
, pp. 363-374
-
-
Irie, H.1
Mori, W.2
-
27
-
-
0020050456
-
Functional and histopathologic changes in the liver during sepsis
-
J.A. Caruana Jr., M. Montes, D.S. Camara, A. Ummer, S.H. Potmesil, and A.A. Gage Functional and histopathologic changes in the liver during sepsis Surg Gynecol Obstet 154 1982 653 656
-
(1982)
Surg Gynecol Obstet
, vol.154
, pp. 653-656
-
-
Caruana, Jr.J.A.1
Montes, M.2
Camara, D.S.3
Ummer, A.4
Potmesil, S.H.5
Gage, A.A.6
-
28
-
-
34548409010
-
Calpain inhibition attenuates iNOS production and midzonal hepatic necrosis in a repeat dose model of endotoxemia in rats
-
R. Rose, A. Banerjee, and S.K. Ramaiah Calpain inhibition attenuates iNOS production and midzonal hepatic necrosis in a repeat dose model of endotoxemia in rats Toxicol Pathol 34 2006 785 794
-
(2006)
Toxicol Pathol
, vol.34
, pp. 785-794
-
-
Rose, R.1
Banerjee, A.2
Ramaiah, S.K.3
-
29
-
-
84886472574
-
Inverse analysis in non-parametric multivariate analyses: Distinguishing groups of associated species which covary coherently across samples
-
P.J. Somerfield, and R.K. Clarke Inverse analysis in non-parametric multivariate analyses: distinguishing groups of associated species which covary coherently across samples J Exp Mar Biol Ecol 449 2013 261 273
-
(2013)
J Exp Mar Biol Ecol
, vol.449
, pp. 261-273
-
-
Somerfield, P.J.1
Clarke, R.K.2
-
30
-
-
0001817172
-
A study of summer foliage insect communities in the Great Smoky Mountains
-
R.H. Whittaker A study of summer foliage insect communities in the Great Smoky Mountains Ecol Monogr 22 1952 1 44
-
(1952)
Ecol Monogr
, vol.22
, pp. 1-44
-
-
Whittaker, R.H.1
-
32
-
-
38849153123
-
-
A. Bush, E.W.F.W. Alton, J.C. Davies, U. Griesenbach, A. Jaffe, Karger New York
-
A. Bush Cystic fibrosis in the 21st century A. Bush, E.W.F.W. Alton, J.C. Davies, U. Griesenbach, A. Jaffe, 2006 Karger New York
-
(2006)
Cystic Fibrosis in the 21st Century
-
-
Bush, A.1
-
34
-
-
0042980340
-
Observations in cystic fibrosis of the pancreas. I. The gallbladder
-
J.R. Esterly, and E.H. Oppenheimer Observations in cystic fibrosis of the pancreas. I. The gallbladder Bull Johns Hopkins Hosp 110 1962 247 255
-
(1962)
Bull Johns Hopkins Hosp
, vol.110
, pp. 247-255
-
-
Esterly, J.R.1
Oppenheimer, E.H.2
-
36
-
-
0020062004
-
Treatment and prognosis of rectal prolapse in cystic fibrosis
-
R.C. Stern, R.J. Izant Jr., T.F. Boat, R.E. Wood, L.W. Matthews, and C.F. Doershuk Treatment and prognosis of rectal prolapse in cystic fibrosis Gastroenterology 82 1982 707 710
-
(1982)
Gastroenterology
, vol.82
, pp. 707-710
-
-
Stern, R.C.1
Izant, Jr.R.J.2
Boat, T.F.3
Wood, R.E.4
Matthews, L.W.5
Doershuk, C.F.6
-
37
-
-
0021779618
-
Bile acid metabolism in children with cystic fibrosis
-
A.M. Weber, and C.C. Roy Bile acid metabolism in children with cystic fibrosis Acta Paediatr Scand Suppl 317 1985 9 15
-
(1985)
Acta Paediatr Scand Suppl
, vol.317
, pp. 9-15
-
-
Weber, A.M.1
Roy, C.C.2
-
38
-
-
4644246657
-
Bacterial overgrowth in the cystic fibrosis transmembrane conductance regulator null mouse small intestine
-
O. Norkina, T.G. Burnett, and R.C. De Lisle Bacterial overgrowth in the cystic fibrosis transmembrane conductance regulator null mouse small intestine Infect Immun 72 2004 6040 6049
-
(2004)
Infect Immun
, vol.72
, pp. 6040-6049
-
-
Norkina, O.1
Burnett, T.G.2
De Lisle, R.C.3
-
39
-
-
33846589817
-
Risk factors for small bowel bacterial overgrowth in cystic fibrosis
-
J.L. Fridge, C. Conrad, L. Gerson, R.O. Castillo, and K. Cox Risk factors for small bowel bacterial overgrowth in cystic fibrosis J Pediatr Gastroenterol Nutr 44 2007 212 218
-
(2007)
J Pediatr Gastroenterol Nutr
, vol.44
, pp. 212-218
-
-
Fridge, J.L.1
Conrad, C.2
Gerson, L.3
Castillo, R.O.4
Cox, K.5
-
40
-
-
84865726240
-
Serial analysis of the gut and respiratory microbiome in cystic fibrosis in infancy: Interaction between intestinal and respiratory tracts and impact of nutritional exposures
-
pii: e00251-12
-
J.C. Madan, D.C. Koestler, B.A. Stanton, L. Davidson, L.A. Moulton, M.L. Housman, J.H. Moore, M.F. Guill, H.G. Morrison, M.L. Sogin, T.H. Hampton, M.R. Karagas, P.E. Palumbo, J.A. Foster, P.L. Hibberd, and G.A. O'Toole Serial analysis of the gut and respiratory microbiome in cystic fibrosis in infancy: interaction between intestinal and respiratory tracts and impact of nutritional exposures MBio 3 2012 pii: e00251-12
-
(2012)
MBio
, vol.3
-
-
Madan, J.C.1
Koestler, D.C.2
Stanton, B.A.3
Davidson, L.4
Moulton, L.A.5
Housman, M.L.6
Moore, J.H.7
Guill, M.F.8
Morrison, H.G.9
Sogin, M.L.10
Hampton, T.H.11
Karagas, M.R.12
Palumbo, P.E.13
Foster, J.A.14
Hibberd, P.L.15
O'Toole, G.A.16
-
41
-
-
77952974496
-
Cystic fibrosis pigs develop lung disease and exhibit defective bacterial eradication at birth
-
D.A. Stoltz, D.K. Meyerholz, A.A. Pezzulo, S. Ramachandran, M.P. Rogan, G.J. Davis, R.A. Hanfland, C. Wohlford-Lenane, C.L. Dohrn, J.A. Bartlett, G.A. Nelson 4th, E.H. Chang, P.J. Taft, P.S. Ludwig, M. Estin, E.E. Hornick, J.L. Launspach, M. Samuel, T. Rokhlina, P.H. Karp, L.S. Ostedgaard, A. Uc, T.D. Starner, A.R. Horswill, K.A. Brogden, R.S. Prather, S.S. Richter, J. Shilyansky, P.B. McCray Jr., J. Zabner, and M.J. Welsh Cystic fibrosis pigs develop lung disease and exhibit defective bacterial eradication at birth Sci Transl Med 2 2010 29ra31
-
(2010)
Sci Transl Med
, vol.2
-
-
Stoltz, D.A.1
Meyerholz, D.K.2
Pezzulo, A.A.3
Ramachandran, S.4
Rogan, M.P.5
Davis, G.J.6
Hanfland, R.A.7
Wohlford-Lenane, C.8
Dohrn, C.L.9
Bartlett, J.A.10
Nelson, G.A.11
Chang, E.H.12
Taft, P.J.13
Ludwig, P.S.14
Estin, M.15
Hornick, E.E.16
Launspach, J.L.17
Samuel, M.18
Rokhlina, T.19
Karp, P.H.20
Ostedgaard, L.S.21
Uc, A.22
Starner, T.D.23
Horswill, A.R.24
Brogden, K.A.25
Prather, R.S.26
Richter, S.S.27
Shilyansky, J.28
McCray Jr., P.B.29
Zabner, J.30
Welsh, M.J.31
more..
-
42
-
-
0035204776
-
Cholangiocyte biology and cystic fibrosis liver disease
-
A.P. Feranchak, and R.J. Sokol Cholangiocyte biology and cystic fibrosis liver disease Semin Liver Dis 21 2001 471 488
-
(2001)
Semin Liver Dis
, vol.21
, pp. 471-488
-
-
Feranchak, A.P.1
Sokol, R.J.2
-
44
-
-
84884211531
-
Evolution of pancreatic function during the first year in infants with cystic fibrosis
-
B.P. O'Sullivan, D. Baker, K.G. Leung, G. Reed, S.S. Baker, and D. Borowitz Evolution of pancreatic function during the first year in infants with cystic fibrosis J Pediatr 162 2013 808 812.e1
-
(2013)
J Pediatr
, vol.162
-
-
O'Sullivan, B.P.1
Baker, D.2
Leung, K.G.3
Reed, G.4
Baker, S.S.5
Borowitz, D.6
-
45
-
-
78951484478
-
Fecal pancreatic elastase-1 levels in older individuals without known gastrointestinal diseases or diabetes mellitus
-
K.H. Herzig, A.K. Purhonen, K.M. Rasanen, J. Idziak, P. Juvonen, R. Phillps, and J. Walkowiak Fecal pancreatic elastase-1 levels in older individuals without known gastrointestinal diseases or diabetes mellitus BMC Geriatr 11 2011 4
-
(2011)
BMC Geriatr
, vol.11
, pp. 4
-
-
Herzig, K.H.1
Purhonen, A.K.2
Rasanen, K.M.3
Idziak, J.4
Juvonen, P.5
Phillps, R.6
Walkowiak, J.7
|