Whole body composition analysis by the BodPod air-displacement plethysmography method in children with Phenylketonuria shows a higher body fat percentage

Journal of Inherited Metabolic Disease

Volumn 33, Issue SUPPL. 3, 2010, Pages

  Albersen, Monique ^a   Bonthuis, Marjolein ^b   De Roos, Nicole M ^c   Van Den Hurk, Dorine A M ^c   Carbasius Weber, Ems ^c   Hendriks, Margriet M W B ^a   De Sain Van Der Velden, Monique G M ^a   De Koning, Tom J ^a   Visser, Gepke ^a  

^a UNIVERSITY MEDICAL CENTER UTRECHT   (Netherlands)

^b WAGENINGEN UNIVERSITY   (Netherlands)

^c UNIVERSITY MEDICAL CENTER UTRECHT   (Netherlands)

Author keywords

[No Author keywords available]

Indexed keywords

AMINO ACID; BIOLOGICAL MARKER; PHENYLALANINE;

ADOLESCENT; AGE; BLOOD; BODY MASS; BODY PLETHYSMOGRAPHY; CASE CONTROL STUDY; CHILD; DEVICES; DIET THERAPY; EQUIPMENT DESIGN; FEMALE; HUMAN; MALE; NEWBORN; NEWBORN SCREENING; OBESITY; PATHOPHYSIOLOGY; PHENYLKETONURIAS; PREDICTIVE VALUE; PROCEDURES; PROTEIN RESTRICTION; SEX DIFFERENCE; STATISTICAL MODEL; WEIGHT GAIN; ARTICLE; EQUIPMENT; METHODOLOGY; PHENYLKETONURIA;

ADIPOSITY; ADOLESCENT; AGE FACTORS; AMINO ACIDS; BIOLOGICAL MARKERS; BODY MASS INDEX; CASE-CONTROL STUDIES; CHILD; DIET, PROTEIN-RESTRICTED; EQUIPMENT DESIGN; FEMALE; HUMANS; INFANT, NEWBORN; LINEAR MODELS; MALE; NEONATAL SCREENING; PHENYLALANINE; PHENYLKETONURIAS; PLETHYSMOGRAPHY, WHOLE BODY; PREDICTIVE VALUE OF TESTS; SEX FACTORS; WEIGHT GAIN;

EID: 84897927846     PISSN: 01418955     EISSN: 15732665     Source Type: Journal    
DOI: 10.1007/s10545-010-9149-8     Document Type: Article

References (16)

1. Acosta PB, Yannicelli S, Singh R et al. (2003) Nutrient intakes and physical growth of children with phenylketonuria undergoing nutrition therapy. J Am Diet Assoc 103(9):1167-1173
2. Allen JR, Baur LA, Waters DL et al. (1996) Body protein in prepubertal children with phenylketonuria. Eur J Clin Nutr 50 (3):178-186
3. Arnold GL, Vladutiu CJ, Kirby RS, Blakely EM, DeLuca JM (2002) Protein insufficiency and linear growth restriction in phenylketonuria. J Pediatr 141(2):243-246
4. Blau N, Erlandsen H (2004) The metabolic and molecular bases of tetrahydrobiopterin-responsive phenylalanine hydroxylase deficiency. Mol Genet Metab 82:101-111
5. Chace DH, Millington DS, Terada N, Kahler SG, Roe CR, Hofman LF (1993) Rapid diagnosis of phenylketonuria by quantitative analysis for phenylalanine and tyrosine in neonatal blood spots by tandem mass spectrometry. Clin Chem 39:66-71
6. DeRoche K, Welsh M (2008) Twenty-five years of research on neurocognitive outcomes in early-treated phenylketonuria: intelligence and executive function. Dev Neuropsychol 33(4):474-504
7. Dobbelaere D, Michaud L, Debrabander A et al. (2003) Evaluation of nutritional status and pathophysiology of growth retardation in patients with phenylketonuria. J Inherit Metab Dis 26 (1):1-11
8. Fields DA, Goran MI, McCrory MA (2002) Body-composition assessment via air-displacement plethysmography in adults and children: a review. Am J Clin Nutr 75(3):453-467
9. Fields DA, Hull HR, Cheline AJ,Yao M, Higgins PB (2004) Child-specific thoracic gas volume prediction equations for air-displacement plethysmography. Obesity Research 12(11):1797-1804
10. Huemer M, Huemer C, Möslinger D, Huter D, Stöckler-Ipsiroglu S (2007) Growth and body composition in children with classical phenylketonuria: results in 34 patients and review of the literature. J Inherit Metab Dis 30(5):694-699
11. Life Measurement Incorporation© (2004) BodPod® Body Composition Tracking System, Operator's Manual PN#2102946 RevF, Concord, CA, USA
12. McBurnie MA, Kronmal RA, Schuett VE, Koch R, Azeng CG (1991) Physical growth of children treated for phenylketonuria. Ann Hum Biol 18(4):357-368
13. Singh AS, Chinapaw MJM, Brug J, Kremers SPJ, Visscher TLS, van Mechelen W (2009) Ethnic differences in BMI among Dutch adolescents: what is the role of screen-viewing, active commuting to school, and consumption of soft drinks and high-caloric snacks? Int J Behav Nutr Phys Act 6 (1):23. Correction: Int J Behav Nutr Phys Act 6(1):40
14. Verkerk PH, van Spronsen FJ, Smit GPA, Sengers RCA (1994) Impaired prenatal and postnatal growth in Dutch patients with phenylketonuria. Arch Dis Child 71:114-118
15. Walter JH, White FJ, Hall SK et al. (2002) How practical are recommendations for dietary control in phenylketonuria? Lancet 360(9326):55-57
16. Walter JH, Lee PJ, Burgard P et al. (2006) Hyperphenylalaninaemia. In: Fernandes J, Saudubray JM, Van den Berghe G, Walter JH (eds) Inborn metabolic diseases: diagnosis and treatment, 4th edn. Springer, Heidelberg, pp 221-231