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Volumn 33, Issue SUPPL. 3, 2010, Pages

Dietary modifications in patients receiving miglustat

Author keywords

[No Author keywords available]

Indexed keywords

1 DEOXYNOJIRIMYCIN; CERAMIDE GLUCOSYLTRANSFERASE; DRUG DERIVATIVE; ENZYME INHIBITOR; GLUCOSYLTRANSFERASE; LACTOSE; MIGLUSTAT;

EID: 84897927240     PISSN: 01418955     EISSN: 15732665     Source Type: Journal    
DOI: 10.1007/s10545-010-9193-4     Document Type: Article
Times cited : (26)

References (10)
  • 2
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    • The role of the iminosugar N-butyldeoxynojirimycin (miglustat) in the management of type i (non-neuronopathic) Gaucher disease: A position statement
    • Cox TM, Aerts JM, Andria G, Beck M, Belmatoug N, Bembi B et al. (2003) The role of the iminosugar N-butyldeoxynojirimycin (miglustat) in the management of type I (non-neuronopathic) Gaucher disease: a position statement. J Inherit Metab Dis 26 (6):513-526
    • (2003) J Inherit Metab Dis , vol.26 , Issue.6 , pp. 513-526
    • Cox, T.M.1    Aerts, J.M.2    Andria, G.3    Beck, M.4    Belmatoug, N.5    Bembi, B.6
  • 3
    • 7244254360 scopus 로고    scopus 로고
    • Sustained therapeutic effects of oral miglustat (Zavesca, N-butyldeoxynojirimycin, OGT 918) in type i Gaucher disease
    • Elstein D, Hollak C, Aerts JM, van Weely S, Maas M, Cox TM et al. (2004) Sustained therapeutic effects of oral miglustat (Zavesca, N- butyldeoxynojirimycin, OGT 918) in type I Gaucher disease. J Inherit Metab Dis 27(6):757-766
    • (2004) J Inherit Metab Dis , vol.27 , Issue.6 , pp. 757-766
    • Elstein, D.1    Hollak, C.2    Aerts, J.M.3    Van Weely, S.4    Maas, M.5    Cox, T.M.6
  • 5
    • 84899072325 scopus 로고    scopus 로고
    • Review of miglustat for clinical management in Gaucher disease type 1
    • Ficicioglu C (2008) Review of miglustat for clinical management in Gaucher disease type 1. Ther Clin Risk Manage 4(2):1-7
    • (2008) Ther Clin Risk Manage , vol.4 , Issue.2 , pp. 1-7
    • Ficicioglu, C.1
  • 6
    • 25844512590 scopus 로고    scopus 로고
    • An open-label, noncomparative study of miglustat in type i Gaucher disease: Efficacy and tolerability over 24 months of treatment
    • Pastores GM, Barnett NL, Kolodny EH (2005) An open-label, noncomparative study of miglustat in type I Gaucher disease: efficacy and tolerability over 24 months of treatment. Clin Ther 27(8):1215-1227
    • (2005) Clin Ther , vol.27 , Issue.8 , pp. 1215-1227
    • Pastores, G.M.1    Barnett, N.L.2    Kolodny, E.H.3
  • 7
    • 34547753513 scopus 로고    scopus 로고
    • Miglustat for treatment of Niemann-Pick C disease: A randomised controlled study
    • Patterson MC, Vecchio D, Prady H, Abel L, Wraith JE (2007) Miglustat for treatment of Niemann-Pick C disease: a randomised controlled study. Lancet Neurol 6(9):765-772
    • (2007) Lancet Neurol , vol.6 , Issue.9 , pp. 765-772
    • Patterson, M.C.1    Vecchio, D.2    Prady, H.3    Abel, L.4    Wraith, J.E.5
  • 8
    • 0028176432 scopus 로고
    • Nbutyldeoxynojirimycin is a novel inhibitor of glycolipid biosynthesis
    • Platt FM, Neises GR, Dwek RA, Butters TD (1994) Nbutyldeoxynojirimycin is a novel inhibitor of glycolipid biosynthesis. J Biol Chem 269(11):8362-8365
    • (1994) J Biol Chem , vol.269 , Issue.11 , pp. 8362-8365
    • Platt, F.M.1    Neises, G.R.2    Dwek, R.A.3    Butters, T.D.4
  • 10
    • 67651242502 scopus 로고    scopus 로고
    • Miglustat in late-onset Tay-Sachs disease: A 12-month, randomized, controlled clinical study with 24 months of extended treatment
    • Shapiro BE, Pastores GM, Gianutsos J, Luzy C, Kolodny EH (2009) Miglustat in late-onset Tay-Sachs disease: a 12-month, randomized, controlled clinical study with 24 months of extended treatment. Genet Med 11(6):425-433
    • (2009) Genet Med , vol.11 , Issue.6 , pp. 425-433
    • Shapiro, B.E.1    Pastores, G.M.2    Gianutsos, J.3    Luzy, C.4    Kolodny, E.H.5


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.