Haploidentical stem cell transplantation in DOCK8 deficiency - Successful control of pre-existing severe viremia with a TCRaß/CD19-depleted graft and antiviral treatment

Clinical Immunology

Volumn 152, Issue 1-2, 2014, Pages 111-114

  Ghosh, Sujal ^a   Schuster, Friedhelm R ^a   Adams, Ortwin ^a   Babor, Florian ^a   Borkhardt, Arndt ^a   Comoli, Patrizia ^b   Handgretinger, Rupert ^c   Lang, Peter ^c   Laws, Hans Jürgen ^a   Siepermann, Meinolf ^a   Meisel, Roland ^a  

^a HEINRICH HEINE UNIVERSITY   (Germany)

^b FONDAZIONE IRCCS POLICLINICO SAN MATTEO   (Italy)

^c UNIVERSITY OF TÜBINGEN   (Germany)

Author keywords

DOCK8 deficiency; HSCT; Hyper IgE; Primary immunodeficiency

Indexed keywords

ANTIVIRUS AGENT; BUDESONIDE; CD19 ANTIGEN; FLUDARABINE; GANCICLOVIR; GRANULOCYTE COLONY STIMULATING FACTOR; MELPHALAN; MYCOPHENOLIC ACID 2 MORPHOLINOETHYL ESTER; T LYMPHOCYTE RECEPTOR BETA CHAIN; THIOTEPA; THYMOCYTE ANTIBODY;

ADOLESCENT; ALLOGENEIC HEMATOPOIETIC STEM CELL TRANSPLANTATION; ANTIVIRAL THERAPY; ASTHMA; ATOPIC DERMATITIS; BURKITT LYMPHOMA; CASE REPORT; CYTOMEGALOVIRUS INFECTION; DEDICATOR OF CYTOKINESIS 8 GENE; DISEASE SEVERITY; DRUG WITHDRAWAL; EPSTEIN BARR VIRUS INFECTION; EXON; FEMALE; FOOD ALLERGY; GENE; GENE DELETION; GENE MUTATION; GENETIC ANALYSIS; GRAFT VERSUS HOST REACTION; HAPLOIDENTICAL ALLOGENEIC HEMATOPOIETIC STEM CELL TRANSPLANTATION; HERPES SIMPLEX; HLA SYSTEM; HUMAN; HYPER IGE SYNDROME; LETTER; LYMPHOCYTE SUBPOPULATION; MENINGOENCEPHALITIS; PAPILLITIS; PNEUMONIA; PRIORITY JOURNAL; PROPHYLAXIS; RECURRENT INFECTION; RESPIRATORY TRACT INFECTION; RETINITIS; VIREMIA; VIRUS LOAD; VISUAL IMPAIRMENT;

DOCK8 DEFICIENCY; HSCT; HYPER IGE; PRIMARY IMMUNODEFICIENCY;

ADOLESCENT; ANTIGENS, CD19; ANTIVIRAL AGENTS; BK VIRUS; FEMALE; GUANINE NUCLEOTIDE EXCHANGE FACTORS; HEMATOPOIETIC STEM CELL TRANSPLANTATION; HUMANS; IMMUNOGLOBULIN G; JOB SYNDROME; LYMPHOCYTE DEPLETION; POLYOMAVIRUS INFECTIONS; RECEPTORS, ANTIGEN, T-CELL, ALPHA-BETA; T-LYMPHOCYTES; TUMOR VIRUS INFECTIONS; TURKEY; VIREMIA;

EID: 84897563653     PISSN: 15216616     EISSN: 15217035     Source Type: Journal    
DOI: 10.1016/j.clim.2014.03.006     Document Type: Letter

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