-
1
-
-
0031458028
-
Incidence, population, and survival of cystic fibrosis in the UK, 1968-95. UK Cystic Fibrosis Survey Management Committee
-
S. Morison, P.A. Lewis, E.C. Coles, D. Geddes, G. Russell, and J.M. Littlewood et al. Incidence, population, and survival of cystic fibrosis in the UK, 1968-95. UK Cystic Fibrosis Survey Management Committee Arch Dis Child 77 1997 493 496
-
(1997)
Arch Dis Child
, vol.77
, pp. 493-496
-
-
Morison, S.1
Lewis, P.A.2
Coles, E.C.3
Geddes, D.4
Russell, G.5
Littlewood, J.M.6
-
3
-
-
0032433707
-
Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease
-
DOI 10.1016/S0092-8674(00)81724-9
-
H. Matsui, B.R. Grubb, R. Tarran, S.H. Randell, J.T. Gatzy, and C.W. Davis et al. Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease Cell 95 1998 1005 1015 (Pubitemid 29019052)
-
(1998)
Cell
, vol.95
, Issue.7
, pp. 1005-1015
-
-
Matsui, H.1
Grubb, B.R.2
Tarran, R.3
Randell, S.H.4
Gatzy, J.T.5
Davis, C.W.6
Boucher, R.C.7
-
4
-
-
23244461620
-
Reduced three-dimensional motility in dehydrated airway mucus prevents neutrophil capture and killing bacteria on airway epithelial surfaces
-
H. Matsui, M.W. Verghese, M. Kesimer, U.E. Schwab, S.H. Randell, and J.K. Sheehan et al. Reduced three-dimensional motility in dehydrated airway mucus prevents neutrophil capture and killing bacteria on airway epithelial surfaces J Immunol 175 2005 1090 1099 (Pubitemid 41094995)
-
(2005)
Journal of Immunology
, vol.175
, Issue.2
, pp. 1090-1099
-
-
Matsui, H.1
Verghese, M.W.2
Kesimer, M.3
Schwab, U.E.4
Randell, S.H.5
Sheehan, J.K.6
Grubb, B.R.7
Boucher, R.C.8
-
5
-
-
0037460729
-
Cystic fibrosis
-
DOI 10.1016/S0140-6736(03)12567-6
-
F. Ratjen, and G. Doring Cystic fibrosis Lancet 361 2003 681 689 (Pubitemid 36246556)
-
(2003)
Lancet
, vol.361
, Issue.9358
, pp. 681-689
-
-
Ratjen, F.1
Doring, G.2
-
8
-
-
0027080197
-
The effects of salmeterol and salbutamol on ciliary beat frequency of cultured human bronchial epithelial cells, in vitro
-
DOI 10.1016/0952-0600(92)90068-R
-
J.L. Devalia, R.J. Sapsford, C. Rusznak, M.J. Toumbis, and R.J. Davies The effects of salmeterol and salbuterol on ciliary beat frequency of cultured human bronchial epithelial cells, in vitro Pulmonary Pharmacol 5 1992 257 263 (Pubitemid 23017755)
-
(1992)
Pulmonary Pharmacology
, vol.5
, Issue.4
, pp. 257-263
-
-
Devalia, J.L.1
Sapsford, R.J.2
Rusznak, C.3
Toumbis, M.J.4
Davies, R.J.5
-
9
-
-
34247390062
-
Association between pulmonary function and sputum biomarkers in cystic fibrosis
-
DOI 10.1164/rccm.200609-1354OC
-
N. Mayer-Hamblett, M.L. Aitken, F.J. Accurso, R.A. Kronmal, M.W. Konstan, and J.L. Burns et al. Association between pulmonary function and sputum biomarkers in cystic fibrosis Am J Respir Crit Care Med 175 2007 822 828 (Pubitemid 46631794)
-
(2007)
American Journal of Respiratory and Critical Care Medicine
, vol.175
, Issue.8
, pp. 822-828
-
-
Mayer-Hamblett, N.1
Aitken, M.L.2
Accurso, F.J.3
Kronmal, R.A.4
Konstan, M.W.5
Burns, J.L.6
Sagel, S.D.7
Ramsey, B.W.8
-
10
-
-
33645096073
-
Reproducibility of a scoring system for computed tomography scanning in cystic fibrosis
-
A.S. Brody, M.R. Kosorok, Z. Li, L.S. Broderick, J.L. Foster, and A. Laxova et al. Reproducibility of a scoring system for computed tomography scanning in cystic fibrosis J Thorac Imaging 21 2006 14 21
-
(2006)
J Thorac Imaging
, vol.21
, pp. 14-21
-
-
Brody, A.S.1
Kosorok, M.R.2
Li, Z.3
Broderick, L.S.4
Foster, J.L.5
Laxova, A.6
-
11
-
-
21744460289
-
Standardisation of spirometry
-
DOI 10.1183/09031936.05.00034805
-
M.R. Miller, J. Hankinson, V. Brusasco, F. Burgos, R. Casaburi, and A. Coates et al. Standardisation of spirometry J Eur Respir 26 2005 319 338 (Pubitemid 41079078)
-
(2005)
European Respiratory Journal
, vol.26
, Issue.2
, pp. 319-338
-
-
Miller, M.R.1
Hankinson, J.2
Brusasco, V.3
Burgos, F.4
Casaburi, R.5
Coates, A.6
Crapo, R.7
Enright, P.8
Van Der Grinten, C.P.M.9
Gustafsson, P.10
Jensen, R.11
Johnson, D.C.12
MacIntrye, N.13
McKay, R.14
Navajas, D.15
Pedersen, O.F.16
Pellegrino, R.17
Viegi, G.18
Wagner, J.19
-
13
-
-
0027752448
-
Pulmonary function growth velocity in children 6 to 18 years of age
-
X. Wang, D.W. Dockery, D. Wypij, D.R. Gold, F.E. Speizer, and J.H. Ware et al. Pulmonary function growth velocity in children 6 to 18 years of age Am Rev Respir Dis 148 1993 1502 1508 (Pubitemid 24002478)
-
(1993)
American Review of Respiratory Disease
, vol.148
, Issue.6
, pp. 1502-1508
-
-
Wang, X.1
Dockery, D.W.2
Wypij, D.3
Gold, D.R.4
Speizer, F.E.5
Ware, J.H.6
Ferris Jr., B.G.7
-
14
-
-
77953306007
-
-
Cystic Fibrosis Foundation Registry Committee; Oct 1
-
Rosenfeld M, Coates A, Corey M, Goss CH, Howard MB, Morgan W, et al. Task Force to Evaluate Choice of Spirometric Reference Equations for the National Patient Registry: Summary and Recommendations. Cystic Fibrosis Foundation Registry Committee; Oct 1, 2005.
-
(2005)
Task Force to Evaluate Choice of Spirometric Reference Equations for the National Patient Registry: Summary and Recommendations
-
-
Rosenfeld, M.1
Coates, A.2
Corey, M.3
Goss, C.H.4
Howard, M.B.5
Morgan, W.6
-
15
-
-
0026504897
-
The effect of aerosol distribution on airway responsiveness to inhaled methacholine in patients with asthma
-
B.L. Laube, P.S. Norman, H.N. Wagner Jr., and G.K. Adams III The effect of aerosol distribution on airway responsiveness to inhaled methacholine in patients with asthma J Allergy Clin Immunol 89 1992 510 518
-
(1992)
J Allergy Clin Immunol
, vol.89
, pp. 510-518
-
-
Laube, B.L.1
Norman, P.S.2
Wagner, Jr.H.N.3
Adams III, G.K.4
-
16
-
-
84878402982
-
Multi-site comparison of mucociliary and cough clearance measures using standardized methods
-
W. Bennett, B.L. Laube, T. Corcoran, P.J. Mogayzel Jr., J. Pilewski, and S. Donaldson Multi-site comparison of mucociliary and cough clearance measures using standardized methods J Aerosol Med Pulm Drug Deliv 26 2013 157 164
-
(2013)
J Aerosol Med Pulm Drug Deliv
, vol.26
, pp. 157-164
-
-
Bennett, W.1
Laube, B.L.2
Corcoran, T.3
Mogayzel, Jr.P.J.4
Pilewski, J.5
Donaldson, S.6
-
17
-
-
84870834612
-
Standardization of techniques for using planar (2D) imaging for aerosol deposition assessment of orally inhaled products
-
S. Newman, W.D. Bennett, M. Biddiscombe, S.G. Devadason, M. Dolovich, and J. Fleming et al. Standardization of techniques for using planar (2D) imaging for aerosol deposition assessment of orally inhaled products J Aerosol Med Pulm Drug Deliv 25 Suppl 1 2012 S10 28
-
(2012)
J Aerosol Med Pulm Drug Deliv
, vol.25
, Issue.SUPPL. 1
, pp. 10-28
-
-
Newman, S.1
Bennett, W.D.2
Biddiscombe, M.3
Devadason, S.G.4
Dolovich, M.5
Fleming, J.6
-
18
-
-
30944452384
-
Mucus clearance and lung function in cystic fibrosis with hypertonic saline
-
DOI 10.1056/NEJMoa043891
-
S.H. Donaldson, W.D. Bennett, K.L. Zeman, M.R. Knowles, R. Tarran, and R.C. Boucher Mucus clearance and lung function in cystic fibrosis with hypertonic saline N Engl J Med 354 2006 241 250 (Pubitemid 43113029)
-
(2006)
New England Journal of Medicine
, vol.354
, Issue.3
, pp. 241-250
-
-
Donaldson, S.H.1
Bennett, W.D.2
Zeman, K.L.3
Knowles, M.R.4
Tarran, R.5
Boucher, R.C.6
-
19
-
-
3242693509
-
High-resolution computed tomography in young patients with cystic fibrosis: Distribution of abnormalities and correlation with pulmonary function tests
-
DOI 10.1016/j.jpeds.2004.02.038, PII S0022347604001684
-
A.S. Brody, J.S. Klein, P.L. Molina, J. Quan, J.A. Bean, and R.W. Wilmott High resolution computed tomography in young patients with cystic fibrosis: distribution of abnormalities and correlation with pulmonary function tests J Pediatr 145 2004 32 38 (Pubitemid 38962449)
-
(2004)
Journal of Pediatrics
, vol.145
, Issue.1
, pp. 32-38
-
-
Brody, A.S.1
Klein, J.S.2
Molina, P.L.3
Quan, J.4
Bean, J.A.5
Wilmott, R.W.6
-
20
-
-
70249089074
-
Association between mucoid Pseudomonas infection and bronchiectasis in children with cystic fibrosis
-
P. Farrell, J. Collins, L. Broderick, M. Rock, Z. Li, and M. Kosorok et al. Association between mucoid Pseudomonas infection and bronchiectasis in children with cystic fibrosis Radiology 252 2009 534 543
-
(2009)
Radiology
, vol.252
, pp. 534-543
-
-
Farrell, P.1
Collins, J.2
Broderick, L.3
Rock, M.4
Li, Z.5
Kosorok, M.6
-
21
-
-
70349831005
-
Australian Respiratory Early Surveillance Team for Cystic Fibrosis (AREST CF). Bronchiectasis in infants and preschool children diagnosed with cystic fibrosis after newboen screening
-
S. Stick, S. Brennan, C. Murray, T. Douglas, B. von Ungern-Sternberg, and L. Garratt et al. Australian Respiratory Early Surveillance Team for Cystic Fibrosis (AREST CF). Bronchiectasis in infants and preschool children diagnosed with cystic fibrosis after newboen screening J Pediatr 155 2009 623 628.e1
-
(2009)
J Pediatr
, vol.155
-
-
Stick, S.1
Brennan, S.2
Murray, C.3
Douglas, T.4
Von Ungern-Sternberg, B.5
Garratt, L.6
-
22
-
-
0027272022
-
Mechanisms of action of Pseudomonas aeruginosa pyocyanin on human ciliary beat in vitro
-
K. Kanthakumar, G. Taylor, K.W. Tsang, D.R. Cundell, A. Rutman, and S. Smith et al. Mechanisms of action of Pseudomonas aeruginosa pyocyanin on human ciliary beat in vitro Infect Immun 61 1993 2848 2853 (Pubitemid 23182278)
-
(1993)
Infection and Immunity
, vol.61
, Issue.7
, pp. 2848-2853
-
-
Kanthakumar, K.1
Taylor, G.2
Tsang, K.W.T.3
Cundell, D.R.4
Rutman, A.5
Smith, S.6
Jeffery, P.K.7
Cole, P.J.8
Wilson, R.9
-
23
-
-
0024391609
-
Effect of pyocyanin and 1-hydroxyphenazine on in vivo tracheal mucus velocity
-
N.C. Munro, A. Barker, A. Rutman, G. Taylor, D. Watson, and W.J. McDonald-Gibson et al. Effect of pyocyanin and 1-hydroxyphenazine on in vivo tracheal mucus velocity J Appl Physiol 67 1989 316 323 (Pubitemid 19196486)
-
(1989)
Journal of Applied Physiology
, vol.67
, Issue.1
, pp. 316-323
-
-
Munro, N.C.1
Barker, A.2
Rutman, A.3
Taylor, G.4
Watson, D.5
McDonald-Gibson, W.J.6
Towart, R.7
Taylor, W.A.8
Wilson, R.9
Cole, P.J.10
-
24
-
-
0035423126
-
The pathobiology of Apergilluis fumigatus
-
J.P. Latge The pathobiology of Apergilluis fumigatus Trends Microbiol 9 2001 382 389
-
(2001)
Trends Microbiol
, vol.9
, pp. 382-389
-
-
Latge, J.P.1
-
25
-
-
0029129327
-
Purification and characterization of factors produced by Aspergillus fumigatus which affect human ciliated respiratory epithelium
-
R. Amitani, G. Taylor, E.-N. Elezis, C. Llewellyn-Jones, J. Mitchell, and F. Kuze et al. Purification and characterization of factors produced by Aspergillus fumigatus which affect human ciliated respiratory epithelium Infect Immun 63 1995 3266 3271
-
(1995)
Infect Immun
, vol.63
, pp. 3266-3271
-
-
Amitani, R.1
Taylor, G.2
Elezis, E.-N.3
Llewellyn-Jones, C.4
Mitchell, J.5
Kuze, F.6
-
26
-
-
0030941873
-
Proteases from Aspergillus fumigatus induce release of proinflammatory cytokines and cell detachment in airway epithelial cell lines
-
J.F.C. Tomee, A.T. Wierenga, P.S. Hiemstra, and H.F. Kauffman Proteases from Aspergillus fumigatus induce release of pro-inflammatory cytokines and cell detachment in airway epithelial cell lines J Infect Dis 176 1997 300 303 (Pubitemid 27272890)
-
(1997)
Journal of Infectious Diseases
, vol.176
, Issue.1
, pp. 300-303
-
-
Tomee, J.F.C.1
Wierenga, A.T.J.2
Hiemstra, P.S.3
Kauffman, H.F.4
|