Pi*Z heterozygous alpha-1 antitrypsin states accelerate parenchymal but not biliary cirrhosis

European Journal of Gastroenterology and Hepatology

Volumn 26, Issue 4, 2014, Pages 412-417

  Cacciottolo, Tessa M ^a   Gelson, William T H ^a   Maguire, Gerald ^b   Davies, Susan E ^b   Griffiths, William J H ^a  

^a ADDENBROOKE S HOSPITAL   (United Kingdom)

^b CAMBRIDGE UNIVERSITY HOSPITALS NHS FOUNDATION TRUST   (United Kingdom)

Author keywords

alpha 1 antitrypsin; heterozygosity; isoelectric focusing parenchymal; periodic acid Schiff

Indexed keywords

ALCOHOL; ALPHA 1 ANTITRYPSIN; CHOLESTEROL ESTER; SERPINA1 PROTEIN, HUMAN;

ADULT; ALCOHOL CONSUMPTION; ARTICLE; AUTOIMMUNE HEPATITIS; BILIARY CIRRHOSIS; BILIARY TRACT DISEASE; COMPARATIVE STUDY; END STAGE LIVER DISEASE; FEMALE; GENE FREQUENCY; GLYCOGEN STORAGE DISEASE; HEMOCHROMATOSIS; HEPATITIS B; HEPATITIS C; HETEROZYGOSITY; HETEROZYGOTE; HUMAN; IMMUNOHISTOCHEMISTRY; ISOELECTRIC FOCUSING; LIVER CIRRHOSIS; LIVER PARENCHYMA; LIVER TRANSPLANTATION; MAJOR CLINICAL STUDY; MALE; MIDDLE AGED; NONALCOHOLIC FATTY LIVER; PHENOTYPE; PREDICTIVE VALUE; PRIORITY JOURNAL; RETROSPECTIVE STUDY; SARCOIDOSIS; SCLEROSING CHOLANGITIS; WILSON DISEASE; ALCOHOL LIVER CIRRHOSIS; BIOPSY; CHEMISTRY; DISEASE COURSE; ENZYMOLOGY; FATTY LIVER; GENETIC PREDISPOSITION; GENETIC SCREENING; GENETICS; LIVER; METABOLISM; PATHOLOGY; PREVALENCE; PROTEIN FOLDING; RISK FACTOR; TIME; UNITED KINGDOM;

ALPHA 1-ANTITRYPSIN; BIOPSY; DISEASE PROGRESSION; ENGLAND; FATTY LIVER; GENE FREQUENCY; GENETIC PREDISPOSITION TO DISEASE; GENETIC TESTING; HETEROZYGOTE; HUMANS; LIVER; LIVER CIRRHOSIS; LIVER CIRRHOSIS, ALCOHOLIC; LIVER CIRRHOSIS, BILIARY; PHENOTYPE; PREDICTIVE VALUE OF TESTS; PREVALENCE; PROTEIN FOLDING; RETROSPECTIVE STUDIES; RISK FACTORS; TIME FACTORS;

EID: 84896391408     PISSN: 0954691X     EISSN: 14735687     Source Type: Journal    
DOI: 10.1097/MEG.0000000000000061     Document Type: Article

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