Cholesterol biosynthesis and ER stress in peroxisome deficiency

Biochimie

Volumn 98, Issue 1, 2014, Pages 75-85

  Faust, Phyllis L ^a   Kovacs, Werner J ^b  

^a Department of Medicine   (United States)

^b ETH ZURICH   (Switzerland)

Author keywords

Cholesterol; ER stress; Integrated stress response; Isoprenoid; Peroxisomes; Pex2; SREBP 2; Unfolded protein response; Zellweger syndrome

Indexed keywords

CHOLESTEROL; ER STRESS; INTEGRATED STRESS RESPONSE; ISOPRENOID; PEROXISOMES; PEX2; SREBP-2; UNFOLDED PROTEIN RESPONSE; ZELLWEGER SYNDROME;

ANIMALS; CHOLESTEROL; ENDOPLASMIC RETICULUM STRESS; FARNESYL-DIPHOSPHATE FARNESYLTRANSFERASE; HUMANS; MEMBRANE PROTEINS; MICE; PEROXISOMES; STEROL REGULATORY ELEMENT BINDING PROTEIN 2; UNFOLDED PROTEIN RESPONSE;

EID: 84895182182     PISSN: 03009084     EISSN: 61831638     Source Type: Journal    
DOI: 10.1016/j.biochi.2013.10.019     Document Type: Review

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