Rapid progression to pulmonary arterial hypertension crisis associated with mixed connective tissue disease in an 11-year-old girl

European Journal of Pediatrics

Volumn 172, Issue 9, 2013, Pages 1263-1265

  Okura, Yuka ^a   Takezaki, Shunichiro ^a   Yamazaki, Yasuhiro ^a   Yamada, Masafumi ^a   Kobayashi, Ichiro ^a   Ariga, Tadashi ^a  

^a HOKKAIDO UNIVERSITY GRADUATE SCHOOL OF MEDICINE   (Japan)

Author keywords

B type natriuretic peptide; Mixed connective tissue disease; Pulmonary arterial hypertension; Pulmonary arterial hypertension crisis; Pulmonary function test

Indexed keywords

AZATHIOPRINE; BERAPROST; BOSENTAN; CYCLOPHOSPHAMIDE; METHYLPREDNISOLONE; PREDNISOLONE; TADALAFIL;

ARTICLE; CASE REPORT; CHILD; DISEASE ASSOCIATION; ECHOCARDIOGRAPHY; FEMALE; HUMAN; LUNG FUNCTION TEST; MEDICAL HISTORY; MIXED CONNECTIVE TISSUE DISEASE; PRIORITY JOURNAL; PULMONARY HYPERTENSION; SCHOOL CHILD;

ACUTE DISEASE; CHILD; DISEASE PROGRESSION; FEMALE; HUMANS; HYPERTENSION, PULMONARY; MIXED CONNECTIVE TISSUE DISEASE;

EID: 84892830133     PISSN: 03406199     EISSN: 14321076     Source Type: Journal    
DOI: 10.1007/s00431-013-2034-3     Document Type: Article

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