Kaposiform lymphangiomatosis: A distinct aggressive lymphatic anomaly

Journal of Pediatrics

Volumn 164, Issue 2, 2014, Pages 383-388

  Croteau, Stacy E ^a,b   Kozakewich, Harry P W ^a,b   Perez Atayde, Antonio R ^a,b   Fishman, Steven J ^a,b   Alomari, Ahmad I ^a,b   Chaudry, Gulraiz ^a,b   Mulliken, John B ^a,b   Trenor III, Cameron C ^a,b  

^a BOSTON CHILDREN S HOSPITAL   (United States)

^b HARVARD MEDICAL SCHOOL   (United States)

Author keywords

Generalized lymphatic anomaly; GLA; Kaposiform hemangioendothelioma; Kaposiform lymphangiomatosis; KHE; KLA; Magnetic resonance imaging; MRI

Indexed keywords

ALPHA INTERFERON; AMINOCAPROIC ACID; CORTICOSTEROID; DOXYCYCLINE; OCTREOTIDE; RAPAMYCIN; THALIDOMIDE; VINCRISTINE; BLEOMYCIN; PEGINTERFERON ALPHA; TALC;

ABDOMINAL DISEASE; ARTICLE; BLOOD CLOTTING DISORDER; CHEST TUBE; CHILD; CLINICAL ARTICLE; CORTICOSTEROID THERAPY; DEATH; ENDOTHELIUM CELL; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; KAPOSIFORM LYMPHANGIOMATOSIS; LIGATION; LIMB DISEASE; LYMPH VESSEL ENDOTHELIUM; LYMPHANGIOMATOSIS; MEDIASTINUM MASS; MORBIDITY; MORTALITY; OBSERVATIONAL STUDY; ONSET AGE; OVERALL SURVIVAL; PERICARDIAL DRAIN; PERICARDIAL EFFUSION; PERICARDIOCENTESIS; PERICARDIOTOMY; PERITONEUM DISEASE; PLEURA EFFUSION; PLEURODESIS; PRESCHOOL CHILD; PRIORITY JOURNAL; PROGNOSIS; REIMPLANTATION; RESPIRATORY TRACT DISEASE; RETROSPECTIVE STUDY; SCLEROTHERAPY; SKIN DISEASE; SPLENECTOMY; SURVIVAL TIME; THORACIC DUCT; THORACOCENTESIS; BLEEDING; CONGENITAL BLOOD VESSEL MALFORMATION; COUGHING; DYSPNEA; ECCHYMOSIS; EPIDURAL HEMATOMA; EPISTAXIS; EXERCISE TOLERANCE; FEMALE; FEVER; FUNCTIONAL STATUS; INTEGUMENT; MALE; NUCLEAR MAGNETIC RESONANCE IMAGING; PERITONEUM; RESPIRATORY FAILURE; SCLERAL HEMORRHAGE; SPLEEN; VAGINA BLEEDING; VISCERA;

GENERALIZED LYMPHATIC ANOMALY; GLA; KAPOSIFORM HEMANGIOENDOTHELIOMA; KAPOSIFORM LYMPHANGIOMATOSIS; KHE; KLA; MAGNETIC RESONANCE IMAGING; MRI;

ADOLESCENT; ADULT; CHILD; CHILD, PRESCHOOL; COMBINED MODALITY THERAPY; DIAGNOSIS, DIFFERENTIAL; ENDOTHELIAL CELLS; FEMALE; HEMANGIOENDOTHELIOMA; HUMANS; INFANT; INFANT, NEWBORN; KASABACH-MERRITT SYNDROME; LYMPH NODES; MAGNETIC RESONANCE IMAGING; MALE; NEOPLASM STAGING; PROGNOSIS; RETROSPECTIVE STUDIES; SARCOMA, KAPOSI; SURVIVAL RATE; UNITED STATES; YOUNG ADULT;

EID: 84892787412     PISSN: 00223476     EISSN: 10976833     Source Type: Journal    
DOI: 10.1016/j.jpeds.2013.10.013     Document Type: Article

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