Modeling of arrhythmogenic right ventricular cardiomyopathy with human induced pluripotent stem cells

Circulation: Cardiovascular Genetics

Volumn 6, Issue 6, 2013, Pages 557-568

  Caspi, Oren ^a,b   Huber, Irit ^a   Gepstein, Amira ^a   Arbel, Gil ^a   Maizels, Leonid ^a   Boulos, Monther ^b   Gepstein, Lior ^a,b  

^a TECHNION ISRAEL INSTITUTE OF TECHNOLOGY   (Israel)

^b RAMBAM MEDICAL CENTER   (Israel)

Author keywords

Arrhythmogenic right ventricular dysplasia; Lipids; Myocytes cardiac; Stem cells

Indexed keywords

6 BROMOINDIRUBIN 3' OXIME; ALKALINE PHOSPHATASE; ALPHA ACTININ; ALPHA FETOPROTEIN; CONNEXIN 43; DESMIN; FAT DROPLET; GLYCOGEN SYNTHASE KINASE 3 INHIBITOR; KRUPPEL LIKE FACTOR 4; NESTIN; OCTAMER TRANSCRIPTION FACTOR 4; ORGANIC CATION TRANSPORTER 3; PEROXISOME PROLIFERATOR ACTIVATED RECEPTOR GAMMA; PLAKOGLOBIN; PLAKOPHILIN; PLAKOPHILIN 2; STAGE SPECIFIC EMBRYO ANTIGEN 4; TRANSCRIPTION FACTOR NANOG; TRANSCRIPTION FACTOR SOX2; TROPONIN I; UNCLASSIFIED DRUG;

ADIPOGENESIS; ADULT; ANIMAL EXPERIMENT; ANIMAL MODEL; APOPTOSIS; ARTICLE; CELL DIFFERENTIATION; CLINICAL ARTICLE; DESMOSOME; DISEASE MODEL; ECHOCARDIOGRAPHY; ECTODERM; ELECTRIC POTENTIAL; ELECTROCARDIOGRAM; EMBRYOID BODY; EMBRYONIC STEM CELL; ENDODERM; FAINTNESS; FAMILY HISTORY; GENE MUTATION; GENETIC ANALYSIS; GERM LAYER; HEART ELECTROPHYSIOLOGY; HEART LEFT BUNDLE BRANCH BLOCK; HEART MUSCLE CELL; HEART PALPITATION; HEART RIGHT VENTRICLE DYSPLASIA; HEART VENTRICLE ARRHYTHMIA; HEART VENTRICLE TACHYCARDIA; HEART VENTRICULOGRAPHY; HUMAN; HUMAN CELL; IMMUNOFLUORESCENCE TEST; IMMUNOHISTOCHEMISTRY; IN VITRO STUDY; LIPID STORAGE; MELANOCYTE; MESODERM; MOUSE; NONHUMAN; NUCLEAR REPROGRAMMING; PHENOTYPE; PLURIPOTENT STEM CELL; PRIORITY JOURNAL; REAL TIME POLYMERASE CHAIN REACTION; SCID BEIGE MOUSE; SKIN FIBROBLAST; STOP CODON; SUDDEN CARDIAC DEATH; T WAVE INVERSION; TRANSMISSION ELECTRON MICROSCOPY; UPREGULATION; WNT SIGNALING PATHWAY; YOUNG ADULT;

ARRHYTHMOGENIC RIGHT VENTRICULAR DYSPLASIA; LIPIDS; MYOCYTES, CARDIAC; STEM CELLS;

APOPTOSIS; ARRHYTHMOGENIC RIGHT VENTRICULAR DYSPLASIA; CELL DIFFERENTIATION; CELLS, CULTURED; CONNEXIN 43; DERMIS; DESMOSOMES; ELECTROCARDIOGRAPHY; FIBROBLASTS; GAMMA CATENIN; GENE EXPRESSION; GLYCOGEN SYNTHASE KINASE 3; HUMANS; IMMUNOHISTOCHEMISTRY; INDOLES; INDUCED PLURIPOTENT STEM CELLS; MICROSCOPY, ELECTRON, TRANSMISSION; MODELS, CARDIOVASCULAR; MUTATION; MYOCYTES, CARDIAC; OXIMES; PLAKOPHILINS; REVERSE TRANSCRIPTASE POLYMERASE CHAIN REACTION;

EID: 84892415382     PISSN: 1942325X     EISSN: 19423268     Source Type: Journal    
DOI: 10.1161/CIRCGENETICS.113.000188     Document Type: Article

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