Usefulness of biochemical parameters in decision-making on the start of emergency treatment in patients with propionic acidemia

Journal of Inherited Metabolic Disease

Volumn 37, Issue 1, 2014, Pages 31-37

  Zwickler, Tamaris ^a   Riderer, Alina ^a   Haege, Gisela ^a   Hoffmann, Georg F ^a   Kölker, Stefan ^a   Burgard, Peter ^a  

^a UNIVERSITY HOSPITAL HEIDELBERG   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

ACID; ACYLCARNITINE; AMMONIA; CARBOXYLIC ACID; CARNITINE; LACTIC ACID; METHYLMALONYL COENZYME A MUTASE;

ADOLESCENT; ADULT; ANION GAP; APPETITE DISORDER; ARTICLE; CHEMICAL ANALYSIS; CHILD; CONSCIOUSNESS DISORDER; EMERGENCY TREATMENT; HUMAN; LEUKOCYTE; MAJOR CLINICAL STUDY; MEDICAL DECISION MAKING; METHYLMALONIC ACIDEMIA; PROPIONIC ACIDEMIA; VOMITING; YOUNG ADULT;

ACID-BASE EQUILIBRIUM; ADOLESCENT; ADULT; AMINO ACID METABOLISM, INBORN ERRORS; AMMONIA; APPETITE; CHILD; CHILD, PRESCHOOL; DECISION MAKING; DECISION SUPPORT TECHNIQUES; EMERGENCY TREATMENT; HUMANS; PROPIONATES; PROPIONIC ACIDEMIA; UNCONSCIOUSNESS; VOMITING; YOUNG ADULT;

EID: 84891803349     PISSN: 01418955     EISSN: 15732665     Source Type: Journal    
DOI: 10.1007/s10545-013-9621-3     Document Type: Article

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