Left atrial enlargement and reduced atrial compliance occurs early in fabry cardiomyopathy

Journal of the American Society of Echocardiography

Volumn 26, Issue 12, 2013, Pages 1415-1423

  Boyd, Anita C ^a   Lo, Queenie ^a   Devine, Kerry ^b   Tchan, Michel C ^b   Sillence, David O ^b   Sadick, Norman ^c   Richards, David A B ^a,c   Thomas, Liza ^a,c  

^a LIVERPOOL HOSPITAL   (Australia)

^b CHILDREN S HOSPITAL AT WESTMEAD   (Australia)

^c UNIVERSITY OF SYDNEY   (Australia)

Author keywords

Atrium; Cardiomyopathy; Echocardiography; Fabry disease

Indexed keywords

ALPHA GALACTOSIDASE;

ADULT; ARTICLE; CARDIOMYOPATHY; CLINICAL ARTICLE; CONTROLLED STUDY; DIASTOLIC BLOOD PRESSURE; DIASTOLIC DYSFUNCTION; ECHOCARDIOGRAPHY; ENZYME REPLACEMENT; FABRY DISEASE; FEMALE; GENE MUTATION; HEART ATRIUM CONTRACTION; HEART ATRIUM ENLARGEMENT; HEART ATRIUM FIBRILLATION; HEART ATRIUM FUNCTION; HEART LEFT ATRIUM; HEART LEFT VENTRICLE EJECTION FRACTION; HEART LEFT VENTRICLE HYPERTROPHY; HEART MUSCLE FIBROSIS; HEART VENTRICLE FIBRILLATION; HEART VENTRICLE SEPTUM; HUMAN; HYPERTROPHIC CARDIOMYOPATHY; LEFT VENTRICULAR DIASTOLIC DYSFUNCTION; MALE; MEAN ARTERIAL PRESSURE; RIGIDITY; SYSTOLIC BLOOD PRESSURE; TISSUE DOPPLER IMAGING;

A SR; ATRIUM; CARDIOMYOPATHY; E SR; EARLY DIASTOLIC STRAIN RATE; ECHOCARDIOGRAPHY; FABRY DISEASE; LA; LATE DIASTOLIC STRAIN RATE; LEFT ATRIAL; LEFT VENTRICULAR; LEFT VENTRICULAR EJECTION FRACTION; LEFT VENTRICULAR HYPERTROPHY; LV; LVEF; LVH; S SR; SYSTOLIC STRAIN RATE;

ADULT; EARLY DIAGNOSIS; ELASTIC MODULUS; FABRY DISEASE; FEMALE; HEART ATRIA; HUMANS; HYPERTROPHY, LEFT VENTRICULAR; MALE; REPRODUCIBILITY OF RESULTS; SENSITIVITY AND SPECIFICITY; TENSILE STRENGTH; VASCULAR RESISTANCE;

EID: 84888433824     PISSN: 08947317     EISSN: 10976795     Source Type: Journal    
DOI: 10.1016/j.echo.2013.08.024     Document Type: Article

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