Structural white matter changes in adolescents and young adults with maple syrup urine disease

Journal of Inherited Metabolic Disease

Volumn 36, Issue 6, 2013, Pages 945-953

  Klee, D ^a   Thimm, E ^a   Wittsack, H J ^a   Schubert, D ^b   Primke, R ^a   Pentang, G ^a   Schaper, J ^a   Modder U ^a   Antoch, A ^a   Wendel, U ^a   Cohnen, M ^b  

^a HEINRICH HEINE UNIVERSITY   (Germany)

^b Lukaskrankenhaus GmbH   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

ALLOISOLEUCINE; BRANCHED CHAIN AMINO ACID; ISOLEUCINE; LEUCINE; VALINE;

ADOLESCENT; ADULT; AMINO ACID BLOOD LEVEL; ANALYTICAL PARAMETERS; APPARENT DIFFUSION COEFFICIENT; ARTICLE; BRAIN STEM; CAPSULA INTERNA; CEREBELLUM; CLINICAL ARTICLE; CONSTANTS AND COEFFICIENTS; CONTROLLED STUDY; DIET THERAPY; DIFFUSION TENSOR IMAGING; DIFFUSION WEIGHTED IMAGING; DISEASE SEVERITY; FEMALE; FRACTIONAL ANISOTROPY; HEMISPHERE; HUMAN; IMAGE ANALYSIS; MALE; MAPLE SYRUP URINE DISEASE; MYELIN DEFICIENCY; NUCLEAR MAGNETIC RESONANCE IMAGING; NUCLEAR MAGNETIC RESONANCE SCANNER; REGIONS OF INTEREST; SIGNAL PROCESSING; SPECTROSCOPY; WHITE MATTER LESION;

ADOLESCENT; ADULT; BRAIN; CASE-CONTROL STUDIES; DIFFUSION MAGNETIC RESONANCE IMAGING; FEMALE; HUMANS; MALE; MAPLE SYRUP URINE DISEASE; NEUROIMAGING; YOUNG ADULT;

EID: 84888199371     PISSN: 01418955     EISSN: 15732665     Source Type: Journal    
DOI: 10.1007/s10545-012-9582-y     Document Type: Article

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