Thalassemias

Pediatric Clinics of North America

Volumn 60, Issue 6, 2013, Pages 1383-1391

  Martin, Alissa ^a   Thompson, Alexis A ^a  

^a CHILDREN'S MEMORIAL HOSPITAL   (United States)

Author keywords

Anemia; Hemoglobinopathies; Iron overload; Thalassemia

Indexed keywords

4 PHENYLBUTYRIC ACID; 5 AZA 2' DEOXYCYTIDINE; ACETYLSALICYLIC ACID; AZACITIDINE; BISPHOSPHONIC ACID DERIVATIVE; DIPYRIDAMOLE; ENDOTHELIN RECEPTOR ANTAGONIST; ERYTHROPOIETIN; HEMOGLOBIN A2; HEMOGLOBIN ALPHA CHAIN; HEMOGLOBIN BETA CHAIN; HEMOGLOBIN E; HEMOGLOBIN F; HEMOGLOBIN H; HYDROXYUREA; PHOSPHODIESTERASE V INHIBITOR; PROSTAGLANDIN RECEPTOR BLOCKING AGENT; SHORT CHAIN FATTY ACID;

ABDOMINAL DISTENSION; ALPHA GLOBIN GENE; ALPHA THALASSEMIA; ANEMIA; AUTOSOMAL RECESSIVE INHERITANCE; BETA GLOBIN GENE; BETA THALASSEMIA; BLOOD CELL COUNT; BLOOD TRANSFUSION; BONE MARROW DISEASE; CALCIUM INTAKE; CHROMOSOME DELETION; DISEASE FREE SURVIVAL; DNA SEQUENCE; DRUG MECHANISM; DYSERYTHROPOIESIS; ELECTROPHORESIS; ETHNIC DIFFERENCE; GENE; GENE MUTATION; GENETIC VARIABILITY; GENOTYPE; GEOGRAPHIC DISTRIBUTION; GRAFT REJECTION; GROWTH RETARDATION; HEMOLYTIC ANEMIA; HEPATOSPLENOMEGALY; HETEROZYGOSITY; HIGH PERFORMANCE LIQUID CHROMATOGRAPHY; HUMAN; HYPERCOAGULABILITY; HYPOGONADOTROPIC HYPOGONADISM; IRON INTAKE; IRRITABILITY; JAUNDICE; OSTEOPENIA; OSTEOPOROSIS; OVERALL SURVIVAL; PATHOPHYSIOLOGY; PHENOTYPIC VARIATION; PREVALENCE; PULMONARY HYPERTENSION; RETICULOCYTE COUNT; REVIEW; RNA SEQUENCE; SPLENECTOMY; SPLENOMEGALY; STEM CELL TRANSPLANTATION; THALASSEMIA; VITAMIN SUPPLEMENTATION;

ANEMIA; HEMOGLOBINOPATHIES; IRON OVERLOAD; THALASSEMIA;

HUMANS; THALASSEMIA; TREATMENT OUTCOME;

EID: 84887608781     PISSN: 00313955     EISSN: 15578240     Source Type: Journal    
DOI: 10.1016/j.pcl.2013.08.008     Document Type: Review

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