Thrombospondin-1 inhibits ADAMTS13 activity in sickle cell disease

Haematologica

Volumn 98, Issue 11, 2013, Pages

  Novelli, Enrico M ^a   Kato, Gregory J ^b   Hildesheim, Mariana E ^c   Barge, Suchitra ^a   Meyer, Michael P ^d   Lozier, Jay ^b   Hassett, Andrea Cortese ^d   Ragni, Margaret V ^a   Isenberg, Jeffrey S ^a   Gladwin, Mark T ^a  

^a UNIVERSITY OF PITTSBURGH SCHOOL OF MEDICINE   (United States)

^b NATIONAL HEART LUNG AND BLOOD INSTITUTE   (United States)

^c NATIONAL INSTITUTES OF HEALTH   (United States)

^d ITXM Diagnostics   (United States)

Author keywords

Acute chest syndrome; ADAMTS13; Sickle cell disease

Indexed keywords

CD47 ANTIGEN; THROMBOSPONDIN 1; VON WILLEBRAND FACTOR; VON WILLEBRAND FACTOR CLEAVING PROTEINASE;

ACUTE CHEST SYNDROME; ADULT; BETA THALASSEMIA; BLOOD CLOTTING; CELL ADHESION; CLINICAL ARTICLE; ENZYME ACTIVITY; ENZYME INHIBITION; ENZYME LINKED IMMUNOSORBENT ASSAY; FEMALE; FLUORESCENCE RESONANCE ENERGY TRANSFER; HUMAN; LETTER; LUNG EMBOLISM; MALE; PROTEIN DEGRADATION; SICKLE CELL ANEMIA; THROMBOCYTOPENIA; THROMBOTIC THROMBOCYTOPENIC PURPURA; WESTERN BLOTTING;

ACUTE CHEST SYNDROME; ADAMTS13; SICKLE CELL DISEASE;

ADAM PROTEINS; ADULT; ANEMIA, SICKLE CELL; COHORT STUDIES; FEMALE; HUMANS; MALE; THROMBOSPONDIN 1; YOUNG ADULT;

EID: 84887007402     PISSN: 03906078     EISSN: 15928721     Source Type: Journal    
DOI: 10.3324/haematol.2013.092635     Document Type: Letter

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