Aging of the Human Neuromuscular System: Patient Vignettes

Muscle Aging, Inclusion-Body Myositis and Myopathies

Volumn , Issue , 2011, Pages 55-80

  Engel, W King ^a   Mahajan, Shalini ^b   Askanas, Valerie ^a  

^a UNIVERSITY OF SOUTHERN CALIFORNIA   (United States)

^b GOOD SAMARITAN HOSPITAL   (United States)

Author keywords

Brain disorder; CSF; EMG; Myopathic disorders; PTHrP; Sausage cramps

Indexed keywords

EID: 84885539845     PISSN: None     EISSN: None     Source Type: Book    
DOI: 10.1002/9781444398311.ch3     Document Type: Chapter

References (23)

1. Engel WK. (1973) "Myopathic EMG" - nonesuch animal. New Engl J Med 289, 485-486.
2. Whitaker JN, Engel WK. (1972) Vascular deposits of immunoglobin and complement in idiopathic inflammatory myopathy. New Engl J Med 286, 333-338.
3. Engel WK, Lichter AS, Galdi AP. (1982) Polymyositis: remarkable response to total body irradiation. Lancet 1, 658.
4. Engel WK, Warmolts JR. (1971) Myasthenia gravis: a new hypothesis of the pathogenesis and a new form of treatment. Ann NY Acad Sci 183, 72-87.
5. Engel WK, Trotter JL, McFarlin DE, McIntosh CXL. (1977) Thymic epithelial cell contains acetylcholine receptor. Lancet 1, 1310-1311.
6. Engel WK. (2010) Multi-microcramps (MMC) syndrome: a new pathogenic concept of subtle lower motor-neuron (LMN) lability causing very disturbing, continuing muscle pains, sometimes gratifying treatable but often misinterpreted as mysterious "fibromyalgia" or "psychogenic". Neurology 74, A465.
7. Mahajan S, Engel WK. (2010) Symptomatic treatment for muscle cramps (an evidence-based review). Letter to the Editor. Neurology 75, 1397-1398.
8. Engel WK, Misra AK, Alexander SJ et al. (1990) Syndrome of continuous motor unit activity responsible to immunosuppression suggests dysimmune pathogenesis. Neurology 40, 118.
9. Warmolts JR, Engel WK. (1972) Open biopsy electromyography. I. Correlation of motor unit behavior with histochemical muscle fiber type inhumanlimb muscle. Arch Neurol 27, 512-517.
10. Engel WK, Prentice AF. (1993) Some polyneuropathies (PNs) in insulin-requiring adult-onset diabetes (IRAOD) can benefit remarkably from anti-dysimmune treatments. Neurology 43, 255-256.
11. Engel WK. (2003) Intravenous immunoglobulin G is remarkably beneficial in chronic immune dysschwannian/ dysneuronal polyneuropathy, diabetes-2 neuropathy, and potentially in severe acute respiratory syndrome. Acta Myol 22, 97-103.
12. Engel WK. (2001) Polyneuropathy in type 2 diabetes mellitus. Lancet 358, 2086.
13. Engel WK. (2006) Longer-term (>3 months), IVIG treatment to optimize clinical benefit and cellular protection usually requires an individualized adjustable schedule not fixed regimentation. Neuromuscul Disord 16, 703-704.
14. Engel, WK (2011) Remarkable benefit persisting undiminshed for 8 years after stopping 14 years of Interferon-a2A (Inf-a) treatment for fever-responsive dysimmune neuropathy (FRDN): possibly a combined antidysimmune plus antiviral effect, and thus a putative model for future "combined antidysimmune" therapies. Neurology 76, A520.
15. Kula RW, Engel WK, Line BR. (1977) Scanning for soft-tissue amyloid. Lancet 1, 92-93.
16. EngelWK, Trotter JL. (1979) Plasma-cell dyscrasic amyloid neuropathy: A parasparafucile phenomenon?. In: Serratrice G, RouxH (eds), Peroneal Atrophies and Related Disorders, MassonPublishingCo, NewYork, pp. 339-347.
17. Yan J, Deng HX, Siddique N et al. (2010) Frameshift and novel mutations in FUS in familial amyotrophic lateral sclerosis and ALS/dementia. Neurology 75, 807-814.
18. Engel WK. (1995) Rapid and continued improvement from intravenous immunoglobulin treatment of asymmetrical chronic progressive muscular atrophy after 19 years of disease progression. Ann Neurol 38, 333-334.
19. Orsini M, Catharino AM, Catharino FM. (2009) Man-in-the-barrel syndrome, a symmetrical proximal brachial amyotrophic displegia related to neuron disease: a survey of nine cases. Rev Assoc Med Bras 55, 712-715.
20. Engel WK. (1987) A simple, low-tech clinical test and treatment for cervical root compression. Ann Neurol 22, 165.
21. Engel WK. (1978) Ponderous-purse disease. Letter to the Editor. New Engl J Med 299, 557.
22. Renton AE, Mejounie E, Waite A, et al. (2011). A hexahucleotide repeat expansion in C90RF72 is the cause of chromosome 9p 21-linked ALS-FTD Neuron. DOI: 10.10.16/j. neuron. 2011.09.010.
23. Engel WK. (1991) RNA metabolism in relation to amyotrophic lateral sclerosis. Adv Neurol 56, 125-153.