Metabolism and energy requirements in pantothenate kinase-associated neurodegeneration

Molecular Genetics and Metabolism

Volumn 110, Issue 3, 2013, Pages 336-341

  Williams, Sarah ^a   Gregory, Allison ^a   Hogarth, Penelope ^a   Hayflick, Susan J ^a   Gillingham, Melanie B ^a  

^a OREGON HEALTH AND SCIENCE UNIVERSITY   (United States)

Author keywords

Coenzyme A; Hallervorden Spatz syndrome; Pantothenate kinase associated neurodegeneration; PKAN; Resting energy expenditure

Indexed keywords

ARACHIDONIC ACID; DOCOSAHEXAENOIC ACID; ESSENTIAL FATTY ACID; IRON; MEVALONIC ACID; SATURATED FATTY ACID; TRANSFERRIN;

ADOLESCENT; ADULT; AGED; ARTICLE; BODY COMPOSITION; CARBOHYDRATE INTAKE; CHILD; CLINICAL ARTICLE; CONTROLLED STUDY; DIETARY INTAKE; DIETARY REFERENCE INTAKE; DISEASE SEVERITY; ENERGY BALANCE; ENERGY EXPENDITURE; ERYTHROCYTE; FEMALE; HUMAN; HUMAN TISSUE; IRON STORAGE; MALE; NEURODEGENERATION WITH BRAIN IRON ACCUMULATION; NUTRITIONAL ASSESSMENT; NUTRITIONAL STATUS; PRIORITY JOURNAL; RESTING ENERGY EXPENDITURE; SCHOOL CHILD; URINE LEVEL;

COENZYME A; HALLERVORDEN-SPATZ SYNDROME; PANTOTHENATE KINASE-ASSOCIATED NEURODEGENERATION; PKAN; RESTING ENERGY EXPENDITURE;

ADOLESCENT; ADULT; AGED; BIOLOGICAL MARKERS; BODY COMPOSITION; CASE-CONTROL STUDIES; CHILD; ENERGY METABOLISM; FEMALE; HUMANS; LIPIDS; MALE; MEVALONIC ACID; MIDDLE AGED; PANTOTHENATE KINASE-ASSOCIATED NEURODEGENERATION; YOUNG ADULT;

EID: 84885426226     PISSN: 10967192     EISSN: 10967206     Source Type: Journal    
DOI: 10.1016/j.ymgme.2013.06.017     Document Type: Article

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