Exercise increases age-related penetrance and arrhythmic risk in arrhythmogenic right ventricular dysplasia/cardiomyopathy-associated desmosomal mutation carriers

Journal of the American College of Cardiology

Volumn 62, Issue 14, 2013, Pages 1290-1297

  James, Cynthia A ^a   Bhonsale, Aditya ^a   Tichnell, Crystal ^a   Murray, Brittney ^a   Russell, Stuart D ^a   Tandri, Harikrishna ^a   Tedford, Ryan J ^a   Judge, Daniel P ^a   Calkins, Hugh ^a  

^a JOHNS HOPKINS UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

arrhythmogenic right ventricular dysplasia; cardiomyopathy; exercise; heart failure; penetrance; ventricular arrhythmias

Indexed keywords

ADULT; ARTICLE; ATHLETE; CARDIOVASCULAR RISK; CHILD; CONTROLLED STUDY; DESMOSOME; DSC2 GENE; DSG2 GENE; DSP GENE; ENDURANCE TRAINING; FOLLOW UP; GENE; GENE MUTATION; HEART FAILURE; HEART RIGHT VENTRICLE DYSPLASIA; HEART VENTRICLE ARRHYTHMIA; HEART VENTRICLE FIBRILLATION; HEART VENTRICLE TACHYCARDIA; HUMAN; JUP GENE; MAJOR CLINICAL STUDY; MALE; PENETRANCE; PHYSICAL ACTIVITY; PKP2 GENE; PRIORITY JOURNAL; SCHOOL CHILD; SURVIVAL RATE;

(STAGE C) HEART FAILURE; 2010 REVISED TASK FORCE CRITERIA; ARRHYTHMOGENIC RIGHT VENTRICULAR DYSPLASIA; ARRHYTHMOGENIC RIGHT VENTRICULAR DYSPLASIA/CARDIOMYOPATHY; ARVD/C; CARDIOMYOPATHY; CI; CONFIDENCE INTERVAL; ECG; ELECTROCARDIOGRAM; EXERCISE; HEART FAILURE; HF; ICD; IMPLANTABLE CARDIOVERTER-DEFIBRILLATOR; INTERQUARTILE RANGE; IQR; ODDS RATIO; OR; PENETRANCE; RIGHT VENTRICULAR; RV; TFC; VENTRICULAR ARRHYTHMIAS; VENTRICULAR TACHYCARDIA/VENTRICULAR FIBRILLATION; VT/VF;

ADULT; ARRHYTHMIAS, CARDIAC; ARRHYTHMOGENIC RIGHT VENTRICULAR DYSPLASIA; DESMOSOMES; ELECTROCARDIOGRAPHY; EXERCISE; FEMALE; FOLLOW-UP STUDIES; HUMANS; MALE; MUTATION; PENETRANCE; PROSPECTIVE STUDIES; RISK FACTORS;

EID: 84884560872     PISSN: 07351097     EISSN: 15583597     Source Type: Journal    
DOI: 10.1016/j.jacc.2013.06.033     Document Type: Article

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