Does the PKU diet contribute to impaired renal function?

Journal of Inherited Metabolic Disease

Volumn 36, Issue 5, 2013, Pages 903-904

  Ney, Denise M ^a  

^a UNIVERSITY OF WISCONSIN MADISON   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

AMINO ACID; CARBON DIOXIDE; EDETATE CHROMIUM; GLYCOPROTEIN; NITROGEN; PHENYLALANINE; UREA;

BONE STRENGTH; COGNITION; COGNITIVE DEFECT; DIET; DIET THERAPY; FLUID INTAKE; GLOMERULUS FILTRATION RATE; HUMAN; KIDNEY DISEASE; KIDNEY FUNCTION; KIDNEY TUMOR; LETTER; NONHUMAN; PHENYLKETONURIA; PROTEIN INTAKE; PROTEINURIA; SOCIAL PSYCHOLOGY; UREA NITROGEN BLOOD LEVEL; URINE VOLUME; WESTERN DIET;

FEMALE; HUMANS; MALE; PHENYLKETONURIAS; RENAL INSUFFICIENCY, CHRONIC;

EID: 84884343104     PISSN: 01418955     EISSN: 15732665     Source Type: Journal    
DOI: 10.1007/s10545-013-9615-1     Document Type: Letter

References (5)

1. Enns GM, Koch R, Brumm V, et al. (2010) Suboptimal outcomes in patients with PKU treated early with diet al.one: revisiting the evidence. Mol Genet Metab 101:99-109
2. Hennermann JB, Roloff S, Gellermann J, et al. (2012) Chronic kidney disease in adolescent and adult patients with phenylketonuria. J Inherit Metab Dis 2012 Nov 09 [epub ahead of print]
3. Solverson P, Murali SG, Brinkman AS, et al. (2012a) Glycomacropeptide, a low-phenylalanine protein isolated from cheese whey, supports growth and attenuates metabolic stress in the murine model of phenylketonuria. Am J Physiol Endocrinol Metab 302:E885-E895
4. Solverson P, Murali SG, Litscher SJ, Blank RD, Ney DM (2012b) Low bone strength is a manifestation of phenylketonuria in mice and is attenuated by a glycomacropeptide diet. PLoS One 7:e45165
5. Van Calcar SC, Macleod EL, Gleason ST, et al. (2009) Improved nutritional management of phenylketonuria by using a diet containing glycomacropeptide compared with amino acids. Am J Clin Nutr 89:1068-1077