Pseudoxanthoma Elasticum: Cardiac Findings in Patients and Abcc6-Deficient Mouse Model

PLoS ONE

Volumn 8, Issue 7, 2013, Pages

  Prunier, Fabrice ^a,b,c   Terrien, Gwenola ^a,b,c   Le Corre, Yannick ^a,c,d   Apana, Ailea L Y ^e   Bière, Loïc ^a,b,c   Kauffenstein, Gilles ^a,d   Furber, Alain ^a,b,c   Bergen, Arthur A B ^f   Gorgels, Theo G M F ^f   Le Saux, Olivier ^e   Leftheriotis, Georges ^a,c,d   Martin, Ludovic ^a,c,d  

^a LUNAM Universite   (France)

^b UNIVERSITÉ D'ANGERS   (France)

^c ANGERS UNIVERSITY HOSPITAL   (France)

^d UNIVERSITÉ D'ANGERS   (France)

^e UNIVERSITY OF HAWAII   (United States)

^f NETHERLANDS INSTITUTE FOR NEUROSCIENCE   (Netherlands)

Author keywords

[No Author keywords available]

Indexed keywords

METHOXY ISOBUTYL ISONITRILE TECHNETIUM TC 99M;

ABCC6 GENE; ADULT; AGED; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; AORTA STENOSIS; ARTICLE; CARDIOVASCULAR MAGNETIC RESONANCE; CARDIOVASCULAR PARAMETERS; COHORT ANALYSIS; CONTROLLED STUDY; DISEASE ASSOCIATION; ECHOCARDIOGRAPHY; ELECTROCARDIOGRAM; FEMALE; GENE; GENE ACTIVITY; GENE FUNCTION; GENETIC ANALYSIS; HEART LEFT VENTRICLE FUNCTION; HEART LEFT VENTRICLE HYPERTROPHY; HEART MUSCLE CONTRACTILITY; HEART VENTRICLE HYPERTROPHY; HEART VENTRICLE SIZE; HUMAN; IMAGE ANALYSIS; MAJOR CLINICAL STUDY; MALE; MITRAL VALVE PROLAPSE; MOUSE; MYOCARDIAL PERFUSION IMAGING; NONHUMAN; PROSPECTIVE STUDY; PSEUDOXANTHOMA ELASTICUM; SINGLE PHOTON EMISSION COMPUTER TOMOGRAPHY; TRANSTHORACIC ECHOCARDIOGRAPHY; TREADMILL EXERCISE; TRICUSPID VALVE DISEASE;

ADULT; ANIMALS; ATP-BINDING CASSETTE TRANSPORTERS; BODY WEIGHT; COHORT STUDIES; CORONARY ARTERY DISEASE; DIASTOLE; DISEASE MODELS, ANIMAL; FEMALE; FIBROSIS; HEART VALVES; HUMANS; MALE; MICE; MIDDLE AGED; MYOCARDIUM; MYOCYTES, CARDIAC; ORGAN SIZE; PSEUDOXANTHOMA ELASTICUM; SYSTOLE; VENTRICULAR FUNCTION;

EID: 84880707305     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0068700     Document Type: Article

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