Abnormal propagation of calcium waves and ultrastructural remodeling in recessive catecholaminergic polymorphic ventricular tachycardia

Circulation Research

Volumn 113, Issue 2, 2013, Pages 142-152

  Liu, Nian ^a   Denegri, Marco ^b   Dun, Wen ^e   Boncompagni, Simona ^d   Lodola, Francesco ^b   Protasi, Feliciano ^d   Napolitano, Carlo ^a,b   Boyden, Penelope A ^e   Priori, Silvia G ^a,b,c  

^a NEW YORK UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b IRCCS   (Italy)

^c UNIVERSITY OF PAVIA   (Italy)

^d UNIVERSITY OF CHIETI   (Italy)

^e Columbia College of Physicians and Surgeons ^*  (United States)

Author keywords

arrhythmias; calcium; calsequestrin; cardiomyopathies; chronic disease; electrophysiology; genetic diseases

Indexed keywords

CALCIUM; CALSEQUESTRIN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CALCIUM HOMEOSTASIS; CALCIUM SIGNALING; CALCIUM TRANSPORT; CATECHOLAMINERGIC POLYMORPHIC VENTRICULAR TACHYCARDIA; CONTROLLED STUDY; HEART ELECTROPHYSIOLOGY; MOUSE; MUSCLE CELL; NONHUMAN; PRIORITY JOURNAL; SARCOPLASMIC RETICULUM; TRANSVERSE TUBULAR SYSTEM; VIRAL GENE DELIVERY SYSTEM;

ARRHYTHMIAS; CALCIUM; CALSEQUESTRIN; CARDIOMYOPATHIES; CHRONIC DISEASE; ELECTROPHYSIOLOGY; GENETIC DISEASES;

ACTION POTENTIALS; ANIMALS; CALCIUM SIGNALING; MICE; MICE, TRANSGENIC; MYOCYTES, CARDIAC; TACHYCARDIA, VENTRICULAR; VENTRICULAR REMODELING;

EID: 84880570426     PISSN: 00097330     EISSN: 15244571     Source Type: Journal    
DOI: 10.1161/CIRCRESAHA.113.301783     Document Type: Article

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