Rapidly progressive amyotrophic lateral sclerosis initially masquerading as a demyelinating neuropathy

Neurophysiologie Clinique

Volumn 43, Issue 3, 2013, Pages 181-187

  Ahdab, R ^a,b   Creange A ^a,c   Saint Val, C ^c   Farhat, W H ^a,b   Lefaucheur, J P ^a,b  

^a UNIVERSITÉ PARIS EST CRÉTEIL   (France)

^b AP HP   (France)

^c Neurologie   (France)

Author keywords

Conduction block; Demyelination; Disease progression; Motor neuron disorder; Neuropathy; Wallerian degeneration

Indexed keywords

RILUZOLE;

ADULT; AMYOTROPHIC LATERAL SCLEROSIS; ARTICLE; CASE REPORT; CLINICAL FEATURE; COMORBIDITY; DEMYELINATING NEUROPATHY; DIAGNOSTIC TEST; DISEASE COURSE; DISEASE DURATION; DISEASE SEVERITY; DRUG WITHDRAWAL; ELECTROMYOGRAPHY; ELECTRONEUROMYOGRAPHY; FATALITY; FEMALE; HUMAN; LIVER FUNCTION; MALE; MOTOR NERVE; MOTOR NERVE CONDUCTION; NERVE FIBER; NUCLEAR MAGNETIC RESONANCE IMAGING; SIDE EFFECT;

ALS; AMYOTROPHIC LATERAL SCLEROSIS; CHRONIC INFLAMMATORY DEMYELINATING POLYNEUROPATHY; CIDP; CMAP; COMPOUND MUSCLE ACTION POTENTIAL; CONDUCTION BLOCK; DÉGÉNÉRESCENCE; DÉMYÉLINISATION; DEMYELINATION; DISEASE PROGRESSION; ELECTRONEUROMYOGRAPHIC EXAMINATION; EMG; ENMG; MAGNETIC RESONANCE IMAGING; MEDICAL RESEARCH COUNCIL; MMN; MOTOR NEURON DISORDER; MRC; MRI; MULTIFOCAL MOTOR NEUROPATHY; NEEDLE ELECTROMYOGRAPHY; NEUROPATHIE; NEUROPATHY; PROGRESSION DE LA MALADIE; WALLERIAN DEGENERATION;

AMYOTROPHIC LATERAL SCLEROSIS; AXONS; CEREBRAL CORTEX; DEMYELINATING DISEASES; DIAGNOSIS, DIFFERENTIAL; ELECTRIC STIMULATION; ELECTROMYOGRAPHY; ELECTROPHYSIOLOGICAL PROCESSES; FEMALE; HUMANS; LOWER EXTREMITY; MALE; MIDDLE AGED; MOTOR NEURONS; MUSCLE WEAKNESS; NERVE DEGENERATION; NEURAL CONDUCTION; NEUROLOGIC EXAMINATION; PERIPHERAL NERVES; SPINAL NERVE ROOTS; UPPER EXTREMITY;

EID: 84880337991     PISSN: 09877053     EISSN: 17697131     Source Type: Journal    
DOI: 10.1016/j.neucli.2013.05.001     Document Type: Article

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