Impaired viability of muscle precursor cells in muscular dystrophy with glycosylation defects and amelioration of its severe phenotype by limited gene expression

Human Molecular Genetics

Volumn 22, Issue 15, 2013, Pages

  Kanagawa, Motoi ^a   Yu, Chih Chieh ^a   Ito, Chiyomi ^a   Fukada, So Ichiro ^b   Hozoji Inada, Masako ^a   Chiyo, Tomoko ^c   Kuga, Atsushi ^a   Matsuo, Megumi ^a   Sato, Kanoko ^a   Yamaguchi, Masahiko ^b   Ito, Takahito ^b   Ohtsuka, Yoshihisa ^a   Katanosaka, Yuki ^d   Miyagoe Suzuki, Yuko ^c   Naruse, Keiji ^d   Kobayashi, Kazuhiro ^a   Okada, Takashi ^c   Takeda, Shin'ichi ^c   Toda, Tatsushi ^a  

^a KOBE UNIVERSITY GRADUATE SCHOOL OF MEDICINE   (Japan)

^b OSAKA UNIVERSITY   (Japan)

^c NATIONAL INSTITUTE OF NEUROSCIENCE   (Japan)

^d OKAYAMA UNIVERSITY   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

ADENOVIRUS VECTOR; DYSTROGLYCAN; FUKUTIN; FCMD PROTEIN, MOUSE; MYOGENIC FACTOR 5; PROTEIN;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; FEMALE; FUKUTIN GENE; GENE; GENE EXPRESSION; GLYCOSYLATION; MALE; MOUSE; MUSCLE ATROPHY; MUSCLE CELL; MUSCLE PRECURSOR CELL; MUSCULAR DYSTROPHY; NONHUMAN; PHENOTYPE; PRIORITY JOURNAL; ANIMAL; CELL SURVIVAL; DISEASE MODEL; GENETICS; KNOCKOUT MOUSE; METABOLISM; MYOBLAST; PATHOLOGY; SKELETAL MUSCLE;

ANIMALS; CELL SURVIVAL; DISEASE MODELS, ANIMAL; DYSTROGLYCANS; GENE EXPRESSION; GLYCOSYLATION; MICE; MICE, KNOCKOUT; MUSCLE, SKELETAL; MUSCULAR DYSTROPHIES; MYOBLASTS; MYOGENIC REGULATORY FACTOR 5; PHENOTYPE; PROTEINS;

EID: 84880256175     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddt157     Document Type: Article

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