Mucopolysaccharidosis Type IIIA presents as a variant of Klüver-Bucy syndrome

Journal of Clinical and Experimental Neuropsychology

Volumn 35, Issue 6, 2013, Pages 608-616

  Potegal, Michael ^a   Yund, Brianna ^b   Rudser, Kyle ^c   Ahmed, Alia ^b   Delaney, Kate ^b   Nestrasil, Igor ^b   Whitley, Chester B ^b   Shapiro, Elsa G ^a  

^a Division of Biostatistics   (United States)

^b UNIVERSITY OF MINNESOTA MEDICAL SCHOOL   (United States)

^c UNIVERSITY OF MINNESOTA   (United States)

Author keywords

Amygdala; Fear conditioning; Orality; Sanfilippo syndrome; Startle

Indexed keywords

ADOLESCENT; AMYGDALOID NUCLEUS; ARTICLE; AVOIDANCE BEHAVIOR; BRAIN CORTEX; BRAIN STEM; CHILD; COMPARATIVE STUDY; COOPERATION; DIFFERENTIAL DIAGNOSIS; DISEASE COURSE; EVOKED BRAIN STEM AUDITORY RESPONSE; EXPLORATORY BEHAVIOR; FEAR; FEMALE; HIPPOCAMPUS; HUMAN; KLUVER BUCY SYNDROME; LEARNING; MALE; NUCLEAR MAGNETIC RESONANCE IMAGING; OBJECT RELATION; PATHOLOGY; PATHOPHYSIOLOGY; PHYSIOLOGY; PRESCHOOL CHILD; PSYCHOLOGICAL ASPECT; SANFILIPPO SYNDROME; SOCIAL ENVIRONMENT; STARTLE REFLEX;

ADOLESCENT; AMYGDALA; ASSOCIATION LEARNING; AVOIDANCE LEARNING; BRAIN STEM; CEREBRAL CORTEX; CHILD; CHILD, PRESCHOOL; COOPERATIVE BEHAVIOR; DIAGNOSIS, DIFFERENTIAL; DISEASE PROGRESSION; EVOKED POTENTIALS, AUDITORY, BRAIN STEM; EXPLORATORY BEHAVIOR; FEAR; FEMALE; HIPPOCAMPUS; HUMANS; KLUVER-BUCY SYNDROME; MAGNETIC RESONANCE IMAGING; MALE; MUCOPOLYSACCHARIDOSIS III; OBJECT ATTACHMENT; SOCIAL ENVIRONMENT; STARTLE REACTION;

EID: 84880224685     PISSN: 13803395     EISSN: 1744411X     Source Type: Journal    
DOI: 10.1080/13803395.2013.804035     Document Type: Article

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