Brain magnetic resonance imaging findings in patients with mucopolysaccharidosis VI

Journal of Inherited Metabolic Disease

Volumn 36, Issue 2, 2013, Pages 357-362

  Azevedo, Ana C M ^a   Artigalás, Osvaldo ^b,c   Vedolin, Leonardo ^d   Komlós, Márcia ^e   Pires, Adriana ^a   Giugliani, Roberto ^a,b   Schwartz, Ida Vanessa D ^a,b  

^a HOSPITAL DE CLÍNICAS DE PORTO ALEGRE   (Brazil)

^b FEDERAL UNIVERSITY OF RIO GRANDE DO SUL   (Brazil)

^c Children s Hospital   (Brazil)

^d HOSPITAL MOINHOS DE VENTO   (Brazil)

^e HOSPITAL MÃE DE DEUS   (Brazil)

Author keywords

[No Author keywords available]

Indexed keywords

GLYCOSAMINOGLYCAN; RECOMBINANT ENZYME;

ADOLESCENT; ADULT; ARTICLE; BRAIN ATROPHY; BRAIN SIZE; BRAIN VENTRICLE DILATATION; BRAZIL; CHILD; CISTERNA MAGNA; CLINICAL ARTICLE; CLINICAL EVALUATION; CONTROLLED STUDY; HUMAN; HYDROCEPHALUS; INTELLIGENCE QUOTIENT; MAROTEAUX LAMY SYNDROME; NUCLEAR MAGNETIC RESONANCE IMAGING; OBSERVATIONAL STUDY; PRESCHOOL CHILD; PROSPECTIVE STUDY; QUALITATIVE ANALYSIS; QUANTITATIVE ANALYSIS; SCHOOL CHILD; URINALYSIS; WHITE MATTER LESION; BRAIN; FEMALE; INTELLIGENCE TEST; MALE; METABOLISM; PATHOLOGY; PROCEDURES; URINE; YOUNG ADULT;

ADOLESCENT; ADULT; BRAIN; CHILD; CHILD, PRESCHOOL; FEMALE; GLYCOSAMINOGLYCANS; HUMANS; INTELLIGENCE TESTS; MAGNETIC RESONANCE IMAGING; MALE; MUCOPOLYSACCHARIDOSIS VI; YOUNG ADULT;

EID: 84879687141     PISSN: 01418955     EISSN: 15732665     Source Type: Journal    
DOI: 10.1007/s10545-012-9559-x     Document Type: Article

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