The outcome of patients with right atrial isomerism is poor

Pediatric Cardiology

Volumn 34, Issue 2, 2013, Pages 302-307

  Eronen, Marianne P ^a   Aittomäki, Kristiina A U ^b   Kajantie, Eero O ^c   Sairanen, Heikki I ^d   Pesonen, Erkki J ^b  

^a SOCIAL INSURANCE INSTITUTION   (Finland)

^b HELSINKI UNIVERSITY CENTRAL HOSPITAL   (Finland)

^c NATIONAL PUBLIC HEALTH INSTITUTE   (Finland)

^d UNIVERSITY OF HELSINKI AND HELSINKI UNIVERSITY HOSPITAL   (Finland)

Author keywords

Asplenia syndrome; Heterotaxia; Outcome; Right isomerism

Indexed keywords

ADOLESCENT; AORTA COARCTATION; ARTICLE; ASPLENIA; ATRIOVENTRICULAR BLOCK; CARDIOVASCULAR MORTALITY; CARDIOVASCULAR SURGERY; CAVOPULMONARY CONNECTION; CHILD; CLEFT LIP PALATE; CLINICAL ARTICLE; COMMON ATRIOVENTRICULAR VALVE; CONGENITAL HEART MALFORMATION; CORONARY ARTERY ANOMALY; COUNSELING; DEXTROCARDIA; DISEASE SEVERITY; DOUBLE OUTLET VENTRICLE; FEMALE; FOLLOW UP; GREAT VESSELS TRANSPOSITION; HEART ARRHYTHMIA; HEART ATRIOVENTRICULAR VALVE; HEART LEFT VENTRICLE OUTFLOW TRACT OBSTRUCTION; HEART OUTFLOW TRACT OBSTRUCTION; HEART RIGHT VENTRICLE DOUBLE OUTLET; HEART SINGLE VENTRICLE; HEART VENTRICLE HYPOPLASIA; HIATUS HERNIA; HUMAN; INFANT; INTESTINE MALROTATION; LUNG ARTERY BANDING; LUNG VEIN DRAINAGE ANOMALY; MALE; NEWBORN; OUTCOME ASSESSMENT; OVERALL SURVIVAL; PREGNANCY; PREGNANCY TERMINATION; PRENATAL DIAGNOSIS; PRESCHOOL CHILD; PROGNOSIS; PULMONARY OUTFLOW TRACT OBSTRUCTION; RIGHT ATRIAL ISOMERISM; SCHOOL CHILD; STOMACH DISEASE; SUPRAVENTRICULAR PREMATURE BEAT; SUPRAVENTRICULAR TACHYCARDIA; SURGICAL TECHNIQUE; SYSTEMIC PULMONARY SHUNT; TREATMENT PLANNING; UNIVERSITY HOSPITAL; VENTRICULOARTERIAL DISCORDANCE;

ADOLESCENT; ADULT; CARDIAC SURGICAL PROCEDURES; CHILD; CHILD, PRESCHOOL; ECHOCARDIOGRAPHY; FEMALE; FINLAND; FOLLOW-UP STUDIES; FORECASTING; GESTATIONAL AGE; HETEROTAXY SYNDROME; HUMANS; INFANT; INFANT, NEWBORN; MALE; PREGNANCY; PREGNANCY COMPLICATIONS, CARDIOVASCULAR; PROGNOSIS; RETROSPECTIVE STUDIES; RISK FACTORS; ULTRASONOGRAPHY, PRENATAL; YOUNG ADULT;

EID: 84879501111     PISSN: 01720643     EISSN: 14321971     Source Type: Journal    
DOI: 10.1007/s00246-012-0445-y     Document Type: Article

References (13)

1. Bernstein D (2000) Heart transplantation in neonates: achievements, controversies and challenges for the future. Neo Rev 1:e152-e159
2. Cheung YF, Cheng VYW, Chau AKT, Chiu CSW et al (2002) Outcome of infants with right atrial isomerism: is prognosis better with normal pulmonary venous drainage. Heart 87:146-152
3. Culbertson DB, George BI, Day RW, Laks H, Williams RG (1992) Factors influencing survival of patients with heterotaxy syndrome undergoing Fontan procedure. J Am Coll Cardiol 20:678-684
4. Eronen M, Kajantie E, Boldt T, Pitkanen O, Aittomaki K (2004) Right atrial isomerism in four siblings. Pediatr Cardiol 25:141-144
5. Eronen M, Aittomäki K, Kajantie E, Sairanen H (2012) Outcome of left atrial isomerism at a single institution. Pediatr Cardiol 33:596-600
6. Freedom RM, Jaeggi ET, Lim JS, Anderson RH (2005) Hearts with isomerism of the right atrial appendages - one of the worst forms of disease in 2005. Cardiol Young 15:554-567
7. Hashmi A, Abu-Sulaiman R, McCrindle BW, Smallhorn JF, Williams WG, Freedom RM (1998) Management and outcomes of right atrial isomerism: a 26-year experience. J Am Coll Cardiol 31(5):1120-1126
8. Ivemark BI (1955) Implications of agenesis of the spleen on the pathogenesis of conotruncus anomalies in childhood: an analysis of the heart malformations in the splenic agenesis syndrome, with fourteen new cases. Acta Paediatr 44(Suppl 104):7-110
9. Kaasinen E, Aittomäki K, Eronen M et al (2010) Recessively inherited right atrial isomerism caused by mutations in growth/differentiation factor 1 (GDF1). Hum Mol Genet 19(14):2747-2753
10. Okita Y, Miki S, Kusuhara K et al (1989) Annuloplastic reconstruction for common atrioventricular valvular regurgitation in right isomerism. Ann Thorac Surg 47:302-304
11. Ota N, Fujimuto Y, Murata M et al (2012) Improving outcomes of the surgical management of right atrial isomerism. Ann Thorac Surg 93(3):832-838
12. Sadiq M, Stumper O, De Giovanni JV, Wright JGC, Sethia B, Brawn WJ et al (1996) Management and outcome of infants and children with right atrial isomerism. Heart 75:314-319
13. Yan YL, Tan KBL, Yeo GSH (2008) Right atrial isomerism preponderance in Asian fetuses. Using the stomach-distance ratio as a possible diagnostic tool for prediction of right atrial isomerism. Ann Acad Med Singapore 37(11):906-912