Selective reduction of bis(monoacylglycero)phosphate ameliorates the storage burden in a THP-1 macrophage model of Gaucher disease

Journal of Lipid Research

Volumn 54, Issue 6, 2013, Pages 1691-1697

  Hein, Leanne K ^a   Duplock, Stephen ^a   Fuller, Maria ^a,b  

^a WOMEN S AND CHILDREN S HOSPITAL   (Australia)

^b UNIVERSITY OF ADELAIDE   (Australia)

Author keywords

[No Author keywords available]

Indexed keywords

BIS(MONOACYLGLYCERO)PHOSPHATE; CERAMIDE DIHEXOSIDE; CERAMIDE TRIHEXOSIDE; DETERGENT; GLUCOSYLCERAMIDE; GLYCEROPHOSPHOLIPID; LINOLEIC ACID; UNCLASSIFIED DRUG;

ARTICLE; CELL STRAIN THP 1; CULTURE MEDIUM; EXTRACTION; GAUCHER DISEASE; HUMAN CELL CULTURE; MACROPHAGE; MASS SPECTROMETRY; PATHOPHYSIOLOGY; PRIORITY JOURNAL; SOLUBILITY; SUCROSE GRADIENT;

DETERGENT-RESISTANT MEMBRANES; FATTY ACIDS; GLUCOSYLCERAMIDE; LYSOSOMAL DISEASE; LYSOSOMAL DYSFUNCTION; LYSOSOMAL STORAGE DISORDER; MASS SPECTROMETRY; MEMBRANE MICRODOMAINS;

CELL LINE, TUMOR; CERAMIDES; GAUCHER DISEASE; GLUCOSYLCERAMIDASE; HUMANS; LINOLEIC ACID; LYSOPHOSPHOLIPIDS; LYSOSOMES; MACROPHAGES; MODELS, BIOLOGICAL; MONOGLYCERIDES; SPHINGOLIPIDS;

EID: 84877913847     PISSN: 00222275     EISSN: 15397262     Source Type: Journal    
DOI: 10.1194/jlr.M038232     Document Type: Article

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