Loss of both phospholipid and triglyceride transfer activities of microsomal triglyceride transfer protein in abetalipoproteinemia

Journal of Lipid Research

Volumn 54, Issue 6, 2013, Pages 1541-1549

  Khatun, Irani ^a,b,c   Walsh, Meghan T ^a,b,c   Hussain, M Mahmood ^b,c  

^a School of Graduate Studies   (United States)

^b Suny Health Science Center   (United States)

^c BioBehavioral Program   (United States)

Author keywords

Apolipoprotein B; Lipoproteins; Mutations

Indexed keywords

APOLIPOPROTEIN B; CALNEXIN; MESSENGER RNA; MICROSOMAL TRIGLYCERIDE TRANSFER PROTEIN; MUTANT PROTEIN; PHOSPHOLIPID; PROTEIN DISULFIDE ISOMERASE; TRIACYLGLYCEROL;

ABETALIPOPROTEINEMIA; ANIMAL CELL; ARTICLE; CELL STRAIN COS7; CELLULAR DISTRIBUTION; CONTROLLED STUDY; LIPID TRANSPORT; MISSENSE MUTATION; NONHUMAN; PATHOPHYSIOLOGY; PRIORITY JOURNAL; PROTEIN ANALYSIS; PROTEIN EXPRESSION; PROTEIN FUNCTION; PROTEIN PROTEIN INTERACTION; PROTEIN SECRETION; STABLE TRANSFECTION;

APOLIPOPROTEIN B; LIPOPROTEINS; MUTATIONS;

ABETALIPOPROTEINEMIA; AMINO ACID SUBSTITUTION; ANIMALS; APOLIPOPROTEINS B; BIOLOGICAL TRANSPORT, ACTIVE; CALNEXIN; CARRIER PROTEINS; CERCOPITHECUS AETHIOPS; COS CELLS; HUMANS; MUTATION, MISSENSE; PHOSPHOLIPIDS; PROTEIN DISULFIDE-ISOMERASES; TRIGLYCERIDES;

EID: 84877898353     PISSN: 00222275     EISSN: 15397262     Source Type: Journal    
DOI: 10.1194/jlr.M031658     Document Type: Article

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