Paediatric presentation and outcome of congenital protein C deficiency in Japan

Haemophilia

Volumn 19, Issue 3, 2013, Pages 378-384

  Ohga, S ^a   Kang, D ^b   Kinjo, T ^a   Ochiai, M ^a   Doi, T ^a   Ishimura, M ^a   Kayamori, Y ^b   Urata, M ^b   Yamamoto, J ^a,c   Suenobu, S I ^d   Kanegane, H ^e   Ikenoue, T ^f   Shirahata, A ^g   Hara, T ^a  

^a KYUSHU UNIVERSITY   (Japan)

^b KYUSHU UNIVERSITY HOSPITAL   (Japan)

^c KYUSHU KOSEI NENKIN HOSPITAL   (Japan)

^d OITA UNIVERSITY   (Japan)

^e UNIVERSITY OF TOYAMA   (Japan)

^f UNIVERSITY OF MIYAZAKI   (Japan)

^g National Hospital Organization   (Japan)

Author keywords

Activated protein C therapy; Intracranial thrombosis haemorrhage; Protein C deficiency; Purpura fulminans

Indexed keywords

ACTIVATED PROTEIN C; ANACT C; UNCLASSIFIED DRUG;

ADOLESCENT; ARTICLE; BLOOD CLOTTING TEST; BRAIN HEMORRHAGE; CHILD; CLINICAL ARTICLE; CLINICAL FEATURE; CONTINUOUS INFUSION; DISEASE COURSE; FEMALE; FULMINATING PURPURA; GENE; GENE MUTATION; GENETIC ANALYSIS; GENOTYPE; HETEROZYGOTE; HOMOZYGOTE; HUMAN; HYDROCEPHALUS; INFANT; JAPAN; MALE; NEUROLOGICAL COMPLICATION; OCCLUSIVE CEREBROVASCULAR DISEASE; ONSET AGE; POSTMARKETING SURVEILLANCE; PRESCHOOL CHILD; PRIORITY JOURNAL; PROC GENE; PROGNOSIS; PROTEIN C DEFICIENCY; RARE DISEASE; SCHOOL CHILD; VENOUS THROMBOEMBOLISM;

ADOLESCENT; ANTICOAGULANTS; CHILD; CHILD, PRESCHOOL; FEMALE; GENOTYPE; HETEROZYGOTE; HOMOZYGOTE; HUMANS; INFANT; INFANT, NEWBORN; JAPAN; MALE; PROTEIN C; PROTEIN C DEFICIENCY; PURPURA FULMINANS; THROMBOSIS; TREATMENT OUTCOME; VENOUS THROMBOEMBOLISM;

EID: 84876811957     PISSN: 13518216     EISSN: 13652516     Source Type: Journal    
DOI: 10.1111/hae.12097     Document Type: Article

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