Impaired regeneration in LGMD2A supported by increased PAX7-positive satellite cell content and muscle-specific microrna dysregulation

Muscle and Nerve

Volumn 47, Issue 5, 2013, Pages 731-739

  Rosales, Xiomara Q ^a,b   Malik, Vinod ^a   Sneh, Amita ^a   Chen, Lei ^a   Lewis, Sarah ^a   Kota, Janaiah ^a   Gastier Foster, Julie M ^a,b   Astbury, Caroline ^a,b   Pyatt, Rob ^a,b   Reshmi, Shalini ^a,b   Rodino Klapac, Louise R ^a,b   Clark, K Reed ^a,b   Mendell, Jerry R ^a,b   Sahenk, Zarife ^a,b  

^a NATIONWIDE CHILDREN S HOSPITAL   (United States)

^b OHIO STATE UNIVERSITY   (United States)

Author keywords

Fibrosis; LGMD2A; MicroRNA; Muscle regeneration; Pax

Indexed keywords

CALPAIN 3; MICRORNA; MICRORNA 1; MICRORNA 133A; MICRORNA 206; TRANSCRIPTION FACTOR PAX7; UNCLASSIFIED DRUG;

ADULT; ARTICLE; CELL DIFFERENTIATION; CELL PROLIFERATION; CELL REGENERATION; CLINICAL ARTICLE; CONTROLLED STUDY; CORRELATION ANALYSIS; DISEASE ACTIVITY; DISEASE DURATION; GENE EXPRESSION; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; IN VITRO STUDY; INFLAMMATION; LIMB GIRDLE MUSCULAR DYSTROPHY; MUSCLE BIOPSY; MUSCLE REGENERATION; NECROSIS; PATHOGENESIS; PRIORITY JOURNAL; SATELLITE CELL;

ADOLESCENT; ADULT; CELL DIFFERENTIATION; CELL PROLIFERATION; CHILD; CHILD, PRESCHOOL; FEMALE; FIBROSIS; HUMANS; MALE; MICRORNAS; MUSCULAR DYSTROPHIES, LIMB-GIRDLE; MYOBLASTS; PAX7 TRANSCRIPTION FACTOR; REGENERATION; SATELLITE CELLS, SKELETAL MUSCLE;

EID: 84876786937     PISSN: 0148639X     EISSN: 10974598     Source Type: Journal    
DOI: 10.1002/mus.23669     Document Type: Article

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