-
1
-
-
33645130994
-
Cystic fibrosis since 1938
-
Davis PB. Cystic fibrosis since 1938. Am J Respir Crit Care Med. 2006;173(5):475-482.
-
(2006)
Am J Respir Crit Care Med.
, vol.173
, Issue.5
, pp. 475-482
-
-
Davis, P.B.1
-
2
-
-
77952315201
-
-
Bethesda MD: ©2011 Cystic Fibrosis Foundation
-
Cystic Fibrosis Foundation Patient Registry. 2009 Annual Data Report. Bethesda MD: ©2011 Cystic Fibrosis Foundation. http://www.cff.org/ UploadedFiles/research/ClinicalResearch/Patient-Registry-Report-2009.pdf.
-
2009 Annual Data Report
-
-
-
3
-
-
0142043977
-
Pathophysiology and management of pulmonary infections in cystic fibrosis
-
Gibson RL, Burns JL, Ramsey BW. Pathophysiology and management of pulmonary infections in cystic fibrosis. Am J Respir Crit Care Med. 2003;168(8):918-951.
-
(2003)
Am J Respir Crit Care Med.
, vol.168
, Issue.8
, pp. 918-951
-
-
Gibson, R.L.1
Burns, J.L.2
Ramsey, B.W.3
-
4
-
-
0036320272
-
Pseudomonas aeruginosa and other predictors of mortality and morbidity in young children with cystic fibrosis
-
Emerson J, Rosenfeld M, McNamara S, Ramsey B, Gibson RL. Pseudomonas aeruginosa and other predictors of mortality and morbidity in young children with cystic fibrosis. Pediatr Pulmonol. 2002;34(2):91-100.
-
(2002)
Pediatr Pulmonol.
, vol.34
, Issue.2
, pp. 91-100
-
-
Emerson, J.1
Rosenfeld, M.2
McNamara, S.3
Ramsey, B.4
Gibson, R.L.5
-
5
-
-
0034764166
-
Early pulmonary infection, inflammation, and clinical outcomes in infants with cystic fibrosis
-
Rosenfeld M, Gibson RL, McNamara S, et al. Early pulmonary infection, inflammation, and clinical outcomes in infants with cystic fibrosis. Pediatr Pulmonol. 2001;32(5):356-366.
-
(2001)
Pediatr Pulmonol.
, vol.32
, Issue.5
, pp. 356-366
-
-
Rosenfeld, M.1
Gibson, R.L.2
McNamara, S.3
-
6
-
-
70350593962
-
Update on antibiotics for infection control in cystic fibrosis
-
Kirkby S, Novak K, McCoy K. Update on antibiotics for infection control in cystic fibrosis. Expert Rev Anti Infect Ther. 2009;7(8):967-980.
-
(2009)
Expert Rev Anti Infect Ther.
, vol.7
, Issue.8
, pp. 967-980
-
-
Kirkby, S.1
Novak, K.2
McCoy, K.3
-
7
-
-
70350446684
-
Cystic fibrosis pulmonary guidelines: Treatment of pulmonary exacerbations
-
Flume PA, Mogayzel PJ Jr, Robinson KA, et al. Cystic fibrosis pulmonary guidelines: treatment of pulmonary exacerbations. Am J Respir Crit Care Med. 2009;180(9):802-808.
-
(2009)
Am J Respir Crit Care Med.
, vol.180
, Issue.9
, pp. 802-808
-
-
Flume, P.A.1
Mogayzel Jr., P.J.2
Robinson, K.A.3
-
8
-
-
33745686502
-
Microbiology, safety, and pharmacokinetics of aztreonam lysinate for inhalation in patients with cystic fibrosis
-
Gibson RL, Retsch-Bogart GZ, Oermann C, et al. Microbiology, safety, and pharmacokinetics of aztreonam lysinate for inhalation in patients with cystic fibrosis. Pediatr Pulmonol. 2006;41(7):656-665.
-
(2006)
Pediatr Pulmonol.
, vol.41
, Issue.7
, pp. 656-665
-
-
Gibson, R.L.1
Retsch-Bogart, G.Z.2
Oermann, C.3
-
10
-
-
0029616734
-
Cystic fibrosis: Genotypic and phenotypic variations
-
Zielenski J, Tsui LC. Cystic fibrosis: genotypic and phenotypic variations. Annu Rev Genet. 1995;29:777-807.
-
(1995)
Annu Rev Genet.
, vol.29
, pp. 777-807
-
-
Zielenski, J.1
Tsui, L.C.2
-
11
-
-
84870746265
-
-
Last updated April 25, 2011. Accessed July 8, 2011
-
Cystic fibrosis mutation database. Available at: http://www.genet. sickkids.on.ca/StatisticsPage.html. Last updated April 25, 2011. Accessed July 8, 2011.
-
Cystic Fibrosis Mutation Database
-
-
-
12
-
-
12844270608
-
Longitudinal development of mucoid Pseudomonas aeruginosa infection and lung disease progression in children with cystic fibrosis
-
Li Z, Kosorok MR, Farrell PM, et al. Longitudinal development of mucoid Pseudomonas aeruginosa infection and lung disease progression in children with cystic fibrosis. JAMA. 2005;293(5):581-588.
-
(2005)
JAMA
, vol.293
, Issue.5
, pp. 581-588
-
-
Li, Z.1
Kosorok, M.R.2
Farrell, P.M.3
-
13
-
-
0034828531
-
Formulation of aerosolized therapeutics
-
Kuhn RJ. Formulation of aerosolized therapeutics. Chest. 2001;120 (Suppl 3):94S-98S.
-
(2001)
Chest
, vol.120
, Issue.SUPPL. 3
-
-
Kuhn, R.J.1
-
14
-
-
0030015857
-
Inhaled antibiotics in cystic fibrosis: A review
-
Toso C, Williams DM, Noone PG. Inhaled antibiotics in cystic fibrosis: a review. Ann Pharmacother. 1996;30(7-8):840-850.
-
(1996)
Ann Pharmacother.
, vol.30
, Issue.7-8
, pp. 840-850
-
-
Toso, C.1
Williams, D.M.2
Noone, P.G.3
-
15
-
-
0033531143
-
Intermittent administration of inhaled tobramycin in patients with cystic fibrosis
-
Cystic Fibrosis Inhaled Tobramycin Study Group
-
Ramsey BW, Pepe MS, Quan JM, et al. Intermittent administration of inhaled tobramycin in patients with cystic fibrosis. Cystic Fibrosis Inhaled Tobramycin Study Group. N Engl J Med. 1999;340(1):23-30.
-
(1999)
N Engl J Med.
, vol.340
, Issue.1
, pp. 23-30
-
-
Ramsey, B.W.1
Pepe, M.S.2
Quan, J.M.3
-
16
-
-
0034835277
-
Microbiological and immunologic considerations with aerosolized drug delivery
-
LiPuma JJ. Microbiological and immunologic considerations with aerosolized drug delivery. Chest. 2001;120(Suppl 3):118S-123S.
-
(2001)
Chest
, vol.120
, Issue.SUPPL. 3
-
-
Lipuma, J.J.1
-
17
-
-
79953284775
-
Inhaled antibiotics for long-term therapy in cystic fibrosis
-
Ryan G, Singh M, Dwan K. Inhaled antibiotics for long-term therapy in cystic fibrosis. Cochrane Database Syst Rev. 2011;(3):CD001021.
-
(2011)
Cochrane Database Syst Rev.
, Issue.3
-
-
Ryan, G.1
Singh, M.2
Dwan, K.3
-
18
-
-
0022776380
-
Single-dose pharmacokinetics of aztreonam in children with cystic fibrosis
-
Reed MD, Aronoff SC, Stern RC, et al. Single-dose pharmacokinetics of aztreonam in children with cystic fibrosis. Pediatr Pulmonol. 1986;2(5):282-286.
-
(1986)
Pediatr Pulmonol.
, vol.2
, Issue.5
, pp. 282-286
-
-
Reed, M.D.1
Aronoff, S.C.2
Stern, R.C.3
-
19
-
-
0036736583
-
A randomised clinical trial of nebulised tobramycin or colistin in cystic fibrosis
-
Hodson ME, Gallagher CG, Govan JR. A randomised clinical trial of nebulised tobramycin or colistin in cystic fibrosis. Eur Respir J. 2002;20(3):658-664.
-
(2002)
Eur Respir J.
, vol.20
, Issue.3
, pp. 658-664
-
-
Hodson, M.E.1
Gallagher, C.G.2
Govan, J.R.3
-
20
-
-
36548999921
-
Compounded colistimethate as possible cause of fatal acute respiratory distress syndrome
-
McCoy KS. Compounded colistimethate as possible cause of fatal acute respiratory distress syndrome. N Engl J Med. 2007;357(22):2310-2311.
-
(2007)
N Engl J Med.
, vol.357
, Issue.22
, pp. 2310-2311
-
-
McCoy, K.S.1
-
21
-
-
0023202934
-
Efficacy of inhaled amikacin as adjunct to intravenous combination therapy (ceftazidime and amikacin) in cystic fibrosis
-
Schaad UB, Wedgwood-Krucko J, Suter S, Kraemer R. Efficacy of inhaled amikacin as adjunct to intravenous combination therapy (ceftazidime and amikacin) in cystic fibrosis. J Pediatr. 1987;111(4):599-605.
-
(1987)
J Pediatr.
, vol.111
, Issue.4
, pp. 599-605
-
-
Schaad, U.B.1
Wedgwood-Krucko, J.2
Suter, S.3
Kraemer, R.4
-
22
-
-
84876211420
-
Treatment of mycobacterium abscessus lung disease: A single center experience
-
Kirkby S, Astor T, Patel A, Novak K, McCoy K. Treatment of mycobacterium abscessus lung disease: A single center experience. Am J Respir Crit Care Med. 2009;179(1):A4085.
-
(2009)
Am J Respir Crit Care Med.
, vol.179
, Issue.1
-
-
Kirkby, S.1
Astor, T.2
Patel, A.3
Novak, K.4
McCoy, K.5
-
23
-
-
0020077544
-
Azthreonam (SQ 26,776), a synthetic monobactam specifically active against aerobic Gram-negative bacteria
-
Sykes RB, Bonner DP, Bush K, Georgopapadakou NH. Azthreonam (SQ 26,776), a synthetic monobactam specifically active against aerobic Gram-negative bacteria. Antimicrob Agents Chemother. 1982;21(1):85-92.
-
(1982)
Antimicrob Agents Chemother.
, vol.21
, Issue.1
, pp. 85-92
-
-
Sykes, R.B.1
Bonner, D.P.2
Bush, K.3
Georgopapadakou, N.H.4
-
25
-
-
0021805738
-
Penetration of aztreonam into human bronchial secretions
-
Bechard DL, Hawkins SS, Dhruv R, Friedhoff LT. Penetration of aztreonam into human bronchial secretions. Antimicrob Agents Chemother. 1985;27(2):263-264.
-
(1985)
Antimicrob Agents Chemother.
, vol.27
, Issue.2
, pp. 263-264
-
-
Bechard, D.L.1
Hawkins, S.S.2
Dhruv, R.3
Friedhoff, L.T.4
-
26
-
-
0021352401
-
In vitro activities of aztreonam, piperacillin, and ticarcillin combined with amikacin against amikacin-resistant Pseudomonas aeruginosa and P. cepacia isolates from children with cystic fibrosis
-
Aronoff SC, Klinger JD. In vitro activities of aztreonam, piperacillin, and ticarcillin combined with amikacin against amikacin-resistant Pseudomonas aeruginosa and P. cepacia isolates from children with cystic fibrosis. Antimicrob Agents Chemother. 1984;25(2):279-280.
-
(1984)
Antimicrob Agents Chemother.
, vol.25
, Issue.2
, pp. 279-280
-
-
Aronoff, S.C.1
Klinger, J.D.2
-
27
-
-
0023176170
-
Efficacy of aztreonam in pulmonary exacerbations of cystic f ibrosis
-
Bosso JA, Black PG, Matsen JM. Efficacy of aztreonam in pulmonary exacerbations of cystic f ibrosis. Pediatr Infect Dis J. 1987;6(4):393-397.
-
(1987)
Pediatr Infect Dis J.
, vol.6
, Issue.4
, pp. 393-397
-
-
Bosso, J.A.1
Black, P.G.2
Matsen, J.M.3
-
28
-
-
0023831069
-
Controlled trial of aztreonam vs tobramycin and azlocillin for acute pulmonary exacerbations of cystic fibrosis
-
Bosso JA, Black PG. Controlled trial of aztreonam vs tobramycin and azlocillin for acute pulmonary exacerbations of cystic fibrosis. Pediatr Infect Dis J. 1988;7(3):171-176.
-
(1988)
Pediatr Infect Dis J.
, vol.7
, Issue.3
, pp. 171-176
-
-
Bosso, J.A.1
Black, P.G.2
-
29
-
-
0016611606
-
Cystic fibrosis: Comparison of two mucolytic drugs for inhalation treatment (acetylcysteine and arginine hydrochloride)
-
Dietzsch HJ, Gottschalk B, Heyne K, Leupoid W, Wunderlich P. Cystic fibrosis: comparison of two mucolytic drugs for inhalation treatment (acetylcysteine and arginine hydrochloride). Pediatrics. 1975;55(1):96-100.
-
(1975)
Pediatrics.
, vol.55
, Issue.1
, pp. 96-100
-
-
Dietzsch, H.J.1
Gottschalk, B.2
Heyne, K.3
Leupoid, W.4
Wunderlich, P.5
-
30
-
-
0031897221
-
Effect of inhaled L-arginine on exhaled nitric oxide in normal and asthmatic subjects
-
Sapienza MA, Kharitonov SA, Horvath I, Chung KF, Barnes PJ. Effect of inhaled L-arginine on exhaled nitric oxide in normal and asthmatic subjects. Thorax. 1998;53(3):172-175.
-
(1998)
Thorax
, vol.53
, Issue.3
, pp. 172-175
-
-
Sapienza, M.A.1
Kharitonov, S.A.2
Horvath, I.3
Chung, K.F.4
Barnes, P.J.5
-
31
-
-
33745761197
-
Inhaled L-arginine improves exhaled nitric oxide and pulmonary function in patients with cystic fibrosis
-
Grasemann H, Kurtz F, Ratjen F. Inhaled L-arginine improves exhaled nitric oxide and pulmonary function in patients with cystic fibrosis. Am J Respir Crit Care Med. 2006;174(2):208-212.
-
(2006)
Am J Respir Crit Care Med.
, vol.174
, Issue.2
, pp. 208-212
-
-
Grasemann, H.1
Kurtz, F.2
Ratjen, F.3
-
32
-
-
38349058630
-
A phase 2 study of aztreonam lysine for inhalation to treat patients with cystic fibrosis and Pseudomonas aeruginosa infection
-
Retsch-Bogart GZ, Burns JL, Otto KL, et al. A phase 2 study of aztreonam lysine for inhalation to treat patients with cystic fibrosis and Pseudomonas aeruginosa infection. Pediatr Pulmonol. 2008;43(1):47-58.
-
(2008)
Pediatr Pulmonol.
, vol.43
, Issue.1
, pp. 47-58
-
-
Retsch-Bogart, G.Z.1
Burns, J.L.2
Otto, K.L.3
-
33
-
-
84876279416
-
-
Princeton, NJ: Bristol-Myers Squibb, January
-
Azactam® package insert. Princeton, NJ: Bristol-Myers Squibb, January 2010.
-
(2010)
Azactam® Package Insert
-
-
-
34
-
-
55549137086
-
Inhaled aztreonam lysine for chronic airway Pseudomonas aeruginosa in cystic fibrosis
-
McCoy KS, Quittner AL, Oermann CM, Gibson RL, Retsch-Bogart GZ, Montgomery AB. Inhaled aztreonam lysine for chronic airway Pseudomonas aeruginosa in cystic fibrosis. Am J Respir Crit Care Med. 2008;178(9):921-928.
-
(2008)
Am J Respir Crit Care Med.
, vol.178
, Issue.9
, pp. 921-928
-
-
McCoy, K.S.1
Quittner, A.L.2
Oermann, C.M.3
Gibson, R.L.4
Retsch-Bogart, G.Z.5
Montgomery, A.B.6
-
35
-
-
65949124667
-
Efficacy and safety of inhaled aztreonam lysine for airway pseudomonas in cystic fibrosis
-
Retsch-Bogart GZ, Quittner AL, Gibson RL, et al. Efficacy and safety of inhaled aztreonam lysine for airway pseudomonas in cystic fibrosis. Chest. 2009;135(5):1223-1232.
-
(2009)
Chest
, vol.135
, Issue.5
, pp. 1223-1232
-
-
Retsch-Bogart, G.Z.1
Quittner, A.L.2
Gibson, R.L.3
-
36
-
-
78449294500
-
An 18-month study of the safety and efficacy of repeated courses of inhaled aztreonam lysine in cystic fibrosis
-
Oermann CM, Retsch-Bogart GZ, Quittner AL, et al. An 18-month study of the safety and efficacy of repeated courses of inhaled aztreonam lysine in cystic fibrosis. Pediatr Pulmonol. 2010;45(11):1121-1134.
-
(2010)
Pediatr Pulmonol.
, vol.45
, Issue.11
, pp. 1121-1134
-
-
Oermann, C.M.1
Retsch-Bogart, G.Z.2
Quittner, A.L.3
-
37
-
-
79958295843
-
Aztreonam for inhalation solution (AZLI) in patients with cystic fibrosis, mild lung impairment, and P. aeruginosa
-
Wainwright CE, Quittner AL, Geller DE, et al. Aztreonam for inhalation solution (AZLI) in patients with cystic fibrosis, mild lung impairment, and P. aeruginosa. J Cyst Fibros. 2011;10(4):234-242.
-
(2011)
J Cyst Fibros.
, vol.10
, Issue.4
, pp. 234-242
-
-
Wainwright, C.E.1
Quittner, A.L.2
Geller, D.E.3
-
38
-
-
3042602206
-
Epidemiology of Burkholderia cepacia complex colonisation in cystic fibrosis patients
-
De Boeck K, Malfroot A, Van Schil L, et al. Epidemiology of Burkholderia cepacia complex colonisation in cystic fibrosis patients. Eur Respir J. 2004;23(6):851-856.
-
(2004)
Eur Respir J.
, vol.23
, Issue.6
, pp. 851-856
-
-
De Boeck, K.1
Malfroot, A.2
Van Schil, L.3
-
39
-
-
3342899443
-
Clinical outcome of Burkholderia cepacia complex infection in cystic fibrosis adults
-
Courtney JM, Dunbar KE, McDowell A, et al. Clinical outcome of Burkholderia cepacia complex infection in cystic fibrosis adults. J Cyst Fibros. 2004;3(2):93-98.
-
(2004)
J Cyst Fibros.
, vol.3
, Issue.2
, pp. 93-98
-
-
Courtney, J.M.1
Dunbar, K.E.2
McDowell, A.3
-
40
-
-
84876244928
-
-
US Food and Drug Administration
-
US Food and Drug Administration. FDA Labeling information- Cayston. FDA Website [online]. Available at: http://www.accessdata.fda.gov/drugsatfda-docs/ label/2010/0508141bl.pdf.
-
FDA Labeling Information- Cayston
-
-
|