Alloantibodies against the B subunit of plasma factor XIII developed in its congenital deficiency

Thrombosis and Haemostasis

Volumn 109, Issue 4, 2013, Pages 661-668

  Wada, Hideho ^a   Souri, Masayoshi ^b   Matsumoto, Rui ^a   Sugihara, Takashi ^a   Ichinose, Akitada ^b  

^a KAWASAKI MEDICAL SCHOOL   (Japan)

^b YAMAGATA UNIVERSITY   (Japan)

Author keywords

Alloantibody; Factor concentrates; Factor XIII resistant state; Factor XIII transglutaminases; Inherited coagulation disorders

Indexed keywords

ALLOANTIBODY; BLOOD CLOTTING FACTOR 13 CONCENTRATE; BLOOD CLOTTING FACTOR 13B; CYCLOSPORIN A; FIBRIN; PREDNISOLONE;

AGED; ANEMIA; ARTICLE; BLOOD CLOTTING FACTOR 13 DEFICIENCY; BLOOD SAMPLING; BONE MARROW BIOPSY; CASE REPORT; DOT HYBRIDIZATION; ENZYME LINKED IMMUNOSORBENT ASSAY; FAMILY STUDY; GASTROINTESTINAL HEMORRHAGE; GENE MUTATION; GINGIVA BLEEDING; HEMORRHOID HEMORRHAGE; HUMAN; MALE; MUSCLE HEMATOMA; MYELODYSPLASTIC SYNDROME; POLYMERASE CHAIN REACTION; PRIORITY JOURNAL; PURPURA; RESTRICTION FRAGMENT LENGTH POLYMORPHISM; THROMBOCYTOPENIA; WESTERN BLOTTING;

AGED; BLOOD COAGULATION; BLOOD COAGULATION TESTS; COAGULANTS; FACTOR XIII; FACTOR XIII DEFICIENCY; GENETIC PREDISPOSITION TO DISEASE; HUMANS; ISOANTIBODIES; MALE; MUTATION; PHENOTYPE; TIME FACTORS; TREATMENT OUTCOME;

EID: 84875963437     PISSN: 03406245     EISSN: None     Source Type: Journal    
DOI: 10.1160/TH12-12-0936     Document Type: Article

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