Dopa-responsive dystonia is caused by particular impairment of nigrostriatal dopamine neurons different from those involved in Parkinson disease: Evidence observed in studies on segawa disease

Neuropediatrics

Volumn 44, Issue 2, 2013, Pages 61-66

  Segawa, Masaya ^a   Nomura, Yoshiko ^a   Hayashi, Masaharu ^b  

^a Segawa Neurological Clinic for Children   (Japan)

^b TOKYO METROPOLITAN INSTITUTE OF MEDICAL SCIENCE   (Japan)

Author keywords

nigrostriatal dopamine neuron; Parkinson disease; Segawa disease

Indexed keywords

DOPA; DOPAMINE; TYROSINE 3 MONOOXYGENASE;

ADULT; AGED; ARTICLE; BRAIN; CASE REPORT; CLINICAL FEATURE; DISEASE DURATION; DOPAMINERGIC NERVE CELL; DYSTONIA; ENZYME ACTIVITY; FEMALE; GENETIC ANALYSIS; HUMAN; IMMUNOHISTOCHEMISTRY; MUSCLE TONE; NEUROCHEMISTRY; NEUROPATHOLOGY; NIGRONEOSTRIATAL SYSTEM; PARKINSON DISEASE; PATHOPHYSIOLOGY; PRIORITY JOURNAL; RISK FACTOR; SEGAWA DISEASE; SYMPTOM; TORTICOLLIS; TREMOR;

AGED, 80 AND OVER; CALCINEURIN; CORPUS STRIATUM; DISEASE PROGRESSION; DOPAMINERGIC NEURONS; DYSTONIC DISORDERS; FEMALE; HUMANS; PARKINSON DISEASE; RECEPTORS, DOPAMINE D2; SUBSTANTIA NIGRA; TYROSINE 3-MONOOXYGENASE;

EID: 84875640753     PISSN: 0174304X     EISSN: 14391899     Source Type: Journal    
DOI: 10.1055/s-0033-1337337     Document Type: Article

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