Successful α1-antitrypsin replacement therapy in a patient with α1-antitrypsin deficiency and granulomatosis with polyangiitis

Rheumatology (United Kingdom)

Volumn 52, Issue 4, 2013, Pages 755-757

  Pérez, José María Hernández ^a   García, Sergio Fumero ^a   Pío, Alberto Alvarez ^a  

^a General Hospital of La Palma   (Spain)

Author keywords

[No Author keywords available]

Indexed keywords

ALPHA 1 ANTITRYPSIN; C REACTIVE PROTEIN; CREATININE; HEMOGLOBIN; METHYLPREDNISOLONE; NEUTROPHIL CYTOPLASMIC ANTIBODY; PREDNISONE; UREA;

ACUTE KIDNEY FAILURE; AGED; ALPHA 1 ANTITRYPSIN DEFICIENCY; ANEMIA; ANOREXIA; ARTHRALGIA; CASE REPORT; COMPUTER ASSISTED TOMOGRAPHY; CORTICOSTEROID THERAPY; CREATININE BLOOD LEVEL; DEHYDRATION; DRUG DOSE REDUCTION; ENZYME REPLACEMENT; FEMALE; FORCED EXPIRATORY VOLUME; GENOTYPE; GRANULOMATOSIS; HEMATURIA; HEMOGLOBIN BLOOD LEVEL; HOSPITAL ADMISSION; HUMAN; HUMAN TISSUE; HYPERTENSION; ISCHEMIC HEART DISEASE; KIDNEY DISEASE; KIDNEY FUNCTION; LETTER; LUNG EMPHYSEMA; MALAISE; MEDICAL HISTORY; MICROSCOPIC POLYANGIITIS; PLEURA EFFUSION; PRIORITY JOURNAL; PROTEINURIA; SKIN BIOPSY; SKIN DEFECT; SUBCUTANEOUS HEMORRHAGE; THORAX RADIOGRAPHY; UREA NITROGEN BLOOD LEVEL; URINE SEDIMENT; VASCULITIS;

AGED, 80 AND OVER; ALPHA 1-ANTITRYPSIN; ALPHA 1-ANTITRYPSIN DEFICIENCY; BIOPSY; CHURG-STRAUSS SYNDROME; DRUG THERAPY, COMBINATION; FEMALE; GLUCOCORTICOIDS; HUMANS; PULMONARY EMPHYSEMA; TOMOGRAPHY, X-RAY COMPUTED; TREATMENT OUTCOME;

EID: 84875614168     PISSN: 14620324     EISSN: 14620332     Source Type: Journal    
DOI: 10.1093/rheumatology/kes233     Document Type: Letter

References (16)

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