Atrophy, fibrosis, and increased PAX7-positive cells in pharyngeal muscles of oculopharyngeal muscular dystrophy patients

Journal of Neuropathology and Experimental Neurology

Volumn 72, Issue 3, 2013, Pages 234-243

  Gidaro, Teresa ^a,b,c   Negroni, Elisa ^a,b,c   Perié, Sophie ^a,b,c,d   Mirabella, Massimiliano ^e   Lainé, Jeanne ^a,b,c   Lacau St Guily, Jean ^a,b,c,d   Butler Browne, Gillian ^a,b,c   Mouly, Vincent ^a,b,c   Trollet, Capucine ^a,b,c  

^a SORBONNE UNIVERSITÉ   (France)

^b Sorbonne Université   (France)

^c CNRS   (France)

^d HÔPITAL TENON   (France)

^e CATHOLIC UNIVERSITY   (Italy)

Author keywords

Atrophy; Fibrosis; Intranuclear inclusion; Oculopharyngeal muscular dystrophy; PABPN1; Pharyngeal muscle; Satellite cells.

Indexed keywords

MYOSIN HEAVY CHAIN ALPHA; TRANSCRIPTION FACTOR PAX7;

ADULT; AGED; ARTICLE; CELL NUCLEUS INCLUSION BODY; CLINICAL ARTICLE; CONTROLLED STUDY; CRICOPHARYNGEUS MUSCLE; DELTOID MUSCLE; FEMALE; FIBROSIS; HUMAN; HUMAN TISSUE; INCLUSION BODY MYOSITIS; MALE; MUSCLE ATROPHY; MUSCLE BIOPSY; MUSCLE REGENERATION; OCULOPHARYNGEAL MUSCULAR DYSTROPHY; PHARYNGEAL MUSCLE; PRIORITY JOURNAL; QUADRICEPS FEMORIS MUSCLE; STERNOCLEIDOMASTOID MUSCLE;

ADULT; AGED; AGED, 80 AND OVER; ATROPHY; FEMALE; FIBROSIS; FLUORESCENT ANTIBODY TECHNIQUE; HUMANS; MALE; MIDDLE AGED; MUSCULAR DYSTROPHY, OCULOPHARYNGEAL; PAX7 TRANSCRIPTION FACTOR; PHARYNGEAL MUSCLES;

EID: 84874649008     PISSN: 00223069     EISSN: 15546578     Source Type: Journal    
DOI: 10.1097/NEN.0b013e3182854c07     Document Type: Article

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