Liver transplantation for urea cycle disorders in pediatric patients: A single-center experience

Pediatric Transplantation

Volumn 17, Issue 2, 2013, Pages 158-167

  Kim, Irene K ^a   Niemi, Anna Kaisa ^b   Krueger, Casey ^b   Bonham, Clark A ^a   Concepcion, Waldo ^a   Cowan, Tina M ^a   Enns, Gregory M ^b   Esquivel, Carlos O ^a  

^a STANFORD UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b STANFORD UNIVERSITY   (United States)

Author keywords

pediatric liver transplantation; urea cycle disorders

Indexed keywords

AMMONIA; ARGININOSUCCINATE LYASE; CARBAMOYL PHOSPHATE SYNTHASE; CITRULLINE; DACLIZUMAB; IMMUNOGLOBULIN; ORNITHINE CARBAMOYLTRANSFERASE; RAPAMYCIN; TACROLIMUS; THYMOCYTE ANTIBODY; UREA;

ADOLESCENT; AMMONIA BLOOD LEVEL; ARGININOSUCCINIC ACID LYASE DEFICIENCY; ARTICLE; BILE DUCT NECROSIS; CARBAMOYL PHOSPHATE SYNTHETASE I DEFICIENCY; CHILD; CHOLESTASIS; CHRONIC GRAFT REJECTION; CHYLOUS EFFUSION; CITRULLINEMIA; CLINICAL ARTICLE; COGNITION; COGNITIVE DEVELOPMENT; DEVELOPMENTAL DISORDER; DIET RESTRICTION; DISEASE SEVERITY; DRUG TOXICITY; EPSTEIN BARR VIRUS INFECTION; FEMALE; FEVER; FOLLOW UP; GRAFT SURVIVAL; HEPATIC ARTERY THROMBOSIS; HERPES SIMPLEX; HUMAN; HYPERAMMONEMIA; IMMUNOSUPPRESSIVE TREATMENT; INFANT; INTESTINE PERFORATION; LENGTH OF STAY; LIVER GRAFT; LIVER GRAFT REJECTION; LIVER SIZE; LIVER TRANSPLANTATION; LIVING DONOR; LONG TERM CARE; MALE; MEDICAL RECORD REVIEW; MONOTHERAPY; NEWBORN SCREENING; ORNITHINE TRANSCARBAMYLASE DEFICIENCY; POSTOPERATIVE COMPLICATION; PRESCHOOL CHILD; RETRANSPLANTATION; ROUX Y ANASTOMOSIS; SCHOOL CHILD; TREATMENT OUTCOME; UREA CYCLE DISORDER;

ADOLESCENT; CHILD; CHILD, PRESCHOOL; DEVELOPMENTAL DISABILITIES; FEMALE; FOLLOW-UP STUDIES; GRAFT SURVIVAL; HUMANS; HYPERAMMONEMIA; INFANT; INFANT, NEWBORN; LIVER TRANSPLANTATION; MALE; RETROSPECTIVE STUDIES; TREATMENT OUTCOME; UREA CYCLE DISORDERS, INBORN;

EID: 84874487768     PISSN: 13973142     EISSN: 13993046     Source Type: Journal    
DOI: 10.1111/petr.12041     Document Type: Article

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