Small heat shock proteins target mutant cystic fibrosis transmembrane conductance regulator for degradation via a small ubiquitin-like modifier-dependent pathway

Molecular Biology of the Cell

Volumn 24, Issue 2, 2013, Pages 74-84

  Ahner, Annette ^a   Gong, Xiaoyan ^a   Schmidt, Bela Z ^a   Peters, Kathryn W ^a   Rabeh, Wael M ^b   Thibodeau, Patrick H ^a   Lukacs, Gergely L ^b   Frizzell, Raymond A ^a  

^a UNIVERSITY OF PITTSBURGH SCHOOL OF MEDICINE   (United States)

^b MCGILL UNIVERSITY   (Canada)

Author keywords

[No Author keywords available]

Indexed keywords

CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; HEAT SHOCK PROTEIN 27; MUTANT PROTEIN; PROTEIN UBC9; SUMO 2 PROTEIN; SUMO 3 PROTEIN; UBIQUITIN PROTEIN LIGASE;

ARTICLE; CONTROLLED STUDY; CYSTIC FIBROSIS; GENE OVEREXPRESSION; HUMAN; HUMAN CELL; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN FOLDING; PROTEIN PROTEIN INTERACTION; PROTEIN TARGETING; SUMOYLATION;

CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; GENE EXPRESSION; GENE KNOCKDOWN TECHNIQUES; HEK293 CELLS; HSP27 HEAT-SHOCK PROTEINS; HUMANS; NUCLEAR PROTEINS; PROTEASOME ENDOPEPTIDASE COMPLEX; PROTEOLYSIS; SEQUENCE DELETION; SUMOYLATION; TRANSCRIPTION FACTORS; UBIQUITIN-CONJUGATING ENZYMES;

EID: 84872286562     PISSN: 10591524     EISSN: 19394586     Source Type: Journal    
DOI: 10.1091/mbc.E12-09-0678     Document Type: Article

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